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ICD-10-CM 2027 diagnosis code

N00.AAcute nephritic syndrome with C3 glomerulonephritis

✓ Billable / specificMCC — major complication/comorbidity

N00.A is a valid, billable ICD-10-CM code for acute nephritic syndrome with c3 glomerulonephritis. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Code last changed in FY2021 (effective October 1, 2020). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About N00.A

N00.A is the ICD-10-CM diagnosis code for acute nephritic syndrome with C3 glomerulonephritis. It belongs to category N00 (acute nephritic syndrome), block N00-N08 (glomerular diseases) and chapter 14 (diseases of the genitourinary system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within N00 (acute nephritic syndrome), N00.A is specifically for acute nephritic syndrome with C3 glomerulonephritis. Related codes cover with minor glomerular abnormality (N00.0), with focal and segmental glomerular lesions (N00.1), with diffuse membranous glomerulonephritis (N00.2), with diffuse mesangial proliferative glomerulonephritis (N00.3), with diffuse endocapillary proliferative glomerulonephritis (N00.4), with diffuse mesangiocapillary glomerulonephritis (N00.5), with dense deposit disease (N00.6), with diffuse crescentic glomerulonephritis (N00.7) and 3 more.

Don't report N00.A together with the conditions in its Excludes1 note: Acute nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N00.6).

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 698 (Other Kidney and Urinary Tract Diagnoses with MCC, relative weight 1.6398), DRG 699 (Other Kidney and Urinary Tract Diagnoses with CC, relative weight 1.0003), DRG 700 (Other Kidney and Urinary Tract Diagnoses without CC/MCC, relative weight 0.6741), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 11 (Diseases and Disorders of the Kidney and Urinary Tract) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It was added in FY2021, effective October 1, 2020.

Coding notes

Applicable toConditions and synonyms classified to this code
  • Acute nephritic syndrome with C3 glomerulopathy, NOS
Excludes1Not coded here — never report together with this code
  • Acute nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N00.6)

Notes that apply from higher levels

Instructions written at a parent level also apply to N00.A.

› From N00 Acute nephritic syndrome
Includes
  • acute glomerular disease
  • acute glomerulonephritis
  • acute nephritis
Excludes1
  • acute tubulo-interstitial nephritis (N10)
  • nephritic syndrome NOS (N05.-)

Broader instructions also apply from N00-N08 Glomerular diseases and Chapter 14: Diseases of the genitourinary system.

Alphabetic index entries

2 entries

Terms in the official ICD-10-CM index that lead to N00.A.

Codes whose notes reference N00.A

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

MDC 15 · Newborns and Other Neonates with Conditions Originating in the Perinatal Period

MDC 15 · Newborns and Other Neonates with Conditions Originating in the Perinatal Period

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2021 (effective 10/1/2020): Added
  • No changes since FY2021.

Common questions about N00.A

Is N00.A billable?

Yes. N00.A is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can N00.A be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict N00.A as a principal diagnosis.

Is N00.A a CC or MCC?

N00.A is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.

What DRG does N00.A group to?

N00.A is used in the MS-DRG v44.0 logic for MS-DRG 698 (Other Kidney and Urinary Tract Diagnoses with MCC), MS-DRG 699 (Other Kidney and Urinary Tract Diagnoses with CC), MS-DRG 700 (Other Kidney and Urinary Tract Diagnoses without CC/MCC), MS-DRG 791 (Prematurity with Major Problems) and MS-DRG 793 (Full Term Neonate with Major Problems). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.