E75.24Niemann-Pick disease

E75.24 is the ICD-10-CM diagnosis code for Niemann-Pick disease. It belongs to category E75 (disorders of sphingolipid metabolism and other lipid storage disorders), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 7 subcodes must be used instead.

Within E75.2 (other sphingolipidosis), E75.24 is specifically for Niemann-Pick disease. Related codes cover Fabry (-Anderson) disease (E75.21), Gaucher disease (E75.22), Krabbe disease (E75.23), Metachromatic leukodystrophy (E75.25), Sulfatase deficiency (E75.26), Pelizaeus-Merzbacher disease (E75.27), Canavan disease (E75.28) and other sphingolipidosis (E75.29).

To report this condition, pick the subcode that matches the documentation: E75.240 (type A), E75.241 (type B), E75.242 (type C), E75.243 (type D), E75.244 (type A/B), E75.248 (disease) and E75.249 (unspecified).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.