ICD-10-CM 2027
ICD-10 code for Variegata parakeratosis
From the official ICD-10-CM alphabetic index entry “Parakeratosis › variegata”. Page updated September 29, 2026.
About coding Variegata parakeratosis
The ICD-10-CM code for Variegata parakeratosis is L41.0 (Pityriasis lichenoides et varioliformis acuta).
Within L41 (parapsoriasis), L41.0 is specifically for pityriasis lichenoides et varioliformis acuta. Related codes cover pityriasis lichenoides chronica (L41.1), small plaque parapsoriasis (L41.3), large plaque parapsoriasis (L41.4), Retiform parapsoriasis (L41.5), other parapsoriasis (L41.8) and unspecified (L41.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 595 (Major Skin Disorders with MCC, relative weight 2.0239) and DRG 596 (Major Skin Disorders without MCC, relative weight 1.1071), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Variegata parakeratosis ICD-10 codes
What is the ICD-10 code for Variegata parakeratosis?
- L41.0 — Pityriasis lichenoides et varioliformis acuta.
Is L41.0 billable?
- Yes. L41.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can L41.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict L41.0 as a principal diagnosis.
Is L41.0 a CC or MCC?
- No. L41.0 is neither a CC nor an MCC under MS-DRG v44.0.