ICD-10-CM 2027
ICD-10 code for van Bogaert-Scherer-Epstein disease or syndrome
From the official ICD-10-CM alphabetic index entry “Van Bogaert-Scherer-Epstein disease or syndrome”. Page updated September 29, 2026.
About coding van Bogaert-Scherer-Epstein disease or syndrome
The ICD-10-CM code for van Bogaert-Scherer-Epstein disease or syndrome is E75.5 (Other lipid storage disorders).
Within E75, choose E75.5 (Other lipid storage disorders) only when documentation doesn't support a more specific option: GM2 gangliosidosis (E75.0), other and unspecified gangliosidosis (E75.1), other sphingolipidosis (E75.2), sphingolipidosis, unspecified (E75.3), Neuronal ceroid lipofuscinosis (E75.4) and lipid storage disorder, unspecified (E75.6).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about van Bogaert-Scherer-Epstein disease or syndrome ICD-10 codes
What is the ICD-10 code for van Bogaert-Scherer-Epstein disease or syndrome?
- E75.5 — Other lipid storage disorders.
Is E75.5 billable?
- Yes. E75.5 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E75.5 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E75.5 as a principal diagnosis.
Is E75.5 a CC or MCC?
- No. E75.5 is neither a CC nor an MCC under MS-DRG v44.0.