ICD-10-CM 2027
ICD-10 code for systemic vasculitis
From the official ICD-10-CM alphabetic index entry “Vasculitis › systemic”. Page updated September 29, 2026.
About coding systemic vasculitis
The ICD-10-CM code for systemic vasculitis is M31.8 (Other specified necrotizing vasculopathies).
Within M31, choose M31.8 (Other specified necrotizing vasculopathies) only when documentation doesn't support a more specific option: hypersensitivity angiitis (M31.0), thrombotic microangiopathy (M31.1), Lethal midline granuloma (M31.2), Wegener's granulomatosis (M31.3), aortic arch syndrome [Takayasu] (M31.4), giant cell arteritis with polymyalgia rheumatica (M31.5), other giant cell arteritis (M31.6), microscopic polyangiitis (M31.7) and 1 more.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 299 (Peripheral Vascular Disorders with MCC, relative weight 1.5842), DRG 300 (Peripheral Vascular Disorders with CC, relative weight 1.0464) and DRG 301 (Peripheral Vascular Disorders without CC/MCC, relative weight 0.7133), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about systemic vasculitis ICD-10 codes
What is the ICD-10 code for systemic vasculitis?
- M31.8 — Other specified necrotizing vasculopathies.
Is M31.8 billable?
- Yes. M31.8 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can M31.8 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict M31.8 as a principal diagnosis.
Is M31.8 a CC or MCC?
- M31.8 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.