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ICD-10-CM 2027

ICD-10 code for syndrome or macroglobulinemia waldenström

C88.0

Waldenstrom macroglobulinemia

Header — needs a more specific code

From the official ICD-10-CM alphabetic index entry “Waldenström › syndrome or macroglobulinemia”. Page updated October 2, 2026.

About coding syndrome or macroglobulinemia waldenström

The ICD-10-CM code for syndrome or macroglobulinemia waldenström is C88.0 (Waldenstrom macroglobulinemia).

Within C88 (malignant immunoproliferative diseases and certain other B-cell lymphomas), C88.0 is specifically for Waldenstrom macroglobulinemia. Related codes cover heavy chain disease (C88.2), immunoproliferative small intestinal disease (C88.3), extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] (C88.4), other malignant immunoproliferative diseases (C88.8) and malignant immunoproliferative disease, unspecified (C88.9).

To report this condition, pick the subcode that matches the documentation: C88.00 (not having achieved remission) and C88.01 (in remission).

Don't report C88.0 together with the conditions in its Excludes1 note: small cell B-cell lymphoma (C83.0).

Don't confuse with (Excludes1 for C88.0)

  • small cell B-cell lymphoma (C83.0)

Common questions about syndrome or macroglobulinemia waldenström ICD-10 codes

What is the ICD-10 code for syndrome or macroglobulinemia waldenström?

C88.0 — Waldenstrom macroglobulinemia (a header code; report a more specific subcode).

Is C88.0 billable?

No. C88.0 is a header code. Report one of its more specific subcodes instead.