ICD-10-CM 2027
ICD-10 code for Sjögren-Larsson syndrome
Other congenital malformation syndromes predominantly associated with short stature
From the official ICD-10-CM alphabetic index entry “Sjögren-Larsson syndrome”. Page updated October 2, 2026.
About coding Sjögren-Larsson syndrome
The ICD-10-CM code for Sjögren-Larsson syndrome is Q87.19 (Other congenital malformation syndromes predominantly associated with short stature).
Within Q87.1, choose Q87.19 (Other congenital malformation syndromes predominantly associated with short stature) only when documentation doesn't support a more specific option: Prader-Willi syndrome (Q87.11).
Use an additional code(s) to identify all associated manifestations.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about Sjögren-Larsson syndrome ICD-10 codes
What is the ICD-10 code for Sjögren-Larsson syndrome?
- Q87.19 — Other congenital malformation syndromes predominantly associated with short stature.
Is Q87.19 billable?
- Yes. Q87.19 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q87.19 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q87.19 as a principal diagnosis.
Is Q87.19 a CC or MCC?
- Q87.19 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.