ICD-10-CM 2027
ICD-10 code for Schwannomatosis
From the official ICD-10-CM alphabetic index entry “Schwannomatosis”. Page updated September 29, 2026.
About coding Schwannomatosis
The ICD-10-CM code for Schwannomatosis is Q85.03 (Schwannomatosis).
Within Q85.0 (neurofibromatosis (nonmalignant)), Q85.03 is specifically for Schwannomatosis. Related codes cover neurofibromatosis, unspecified (Q85.00), neurofibromatosis, type 1 (Q85.01), neurofibromatosis, type 2 (Q85.02) and other neurofibromatosis (Q85.09).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Schwannomatosis ICD-10 codes
What is the ICD-10 code for Schwannomatosis?
- Q85.03 — Schwannomatosis.
Is Q85.03 billable?
- Yes. Q85.03 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q85.03 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q85.03 as a principal diagnosis.
Is Q85.03 a CC or MCC?
- No. Q85.03 is neither a CC nor an MCC under MS-DRG v44.0.