ICD-10 code for right heart syndrome hypoplasia

The ICD-10-CM code for right heart syndrome hypoplasia is Q22.6 (Hypoplastic right heart syndrome).

Within Q22 (congenital malformations of pulmonary and tricuspid valves), Q22.6 is specifically for Hypoplastic right heart syndrome. Related codes cover pulmonary valve atresia (Q22.0), congenital pulmonary valve stenosis (Q22.1), congenital pulmonary valve insufficiency (Q22.2), other congenital malformations of pulmonary valve (Q22.3), congenital tricuspid stenosis (Q22.4), Ebstein's anomaly (Q22.5), other congenital malformations of tricuspid valve (Q22.8) and congenital malformation of tricuspid valve, unspecified (Q22.9).

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.