ICD-10-CM 2027
ICD-10 code for pigmentation anomaly
From the official ICD-10-CM alphabetic index entry “Anomaly, anomalous (congenital) (unspecified type) › pigmentation”. Page updated September 29, 2026.
About coding pigmentation anomaly
The ICD-10-CM code for pigmentation anomaly is L81.9 (Disorder of pigmentation, unspecified). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on L81.9.
Within L81, choose L81.9 (Disorder of pigmentation, unspecified) only when documentation doesn't support a more specific option: postinflammatory hyperpigmentation (L81.0), Chloasma (L81.1), Freckles (L81.2), cafe au lait spots (L81.3), other melanin hyperpigmentation (L81.4), Leukoderma, not elsewhere classified (L81.5), other disorders of diminished melanin formation (L81.6), pigmented purpuric dermatosis (L81.7) and 1 more.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728), DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772) and DRG 795 (Normal Newborn, relative weight 0.2022), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific pigmentation anomaly codes (official index)
- congenital Q82.8 — Other specified congenital malformations of skin
Common questions about pigmentation anomaly ICD-10 codes
What is the ICD-10 code for pigmentation anomaly?
- L81.9 — Disorder of pigmentation, unspecified. More specific codes apply when the documentation supports them: Q82.8.
What is the ICD-10 code for congenital pigmentation anomaly?
- Q82.8 — Other specified congenital malformations of skin.
Is L81.9 billable?
- Yes. L81.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can L81.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict L81.9 as a principal diagnosis.
Is L81.9 a CC or MCC?
- No. L81.9 is neither a CC nor an MCC under MS-DRG v44.0.