ICD-10 code for pemphigus

The ICD-10-CM code for pemphigus is L10.9 (Pemphigus, unspecified). The official index lists 15 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on L10.9.

Within L10, choose L10.9 (unspecified) only when documentation doesn't support a more specific option: vulgaris (L10.0), vegetans (L10.1), foliaceous (L10.2), Brazilian pemphigus [fogo selvagem] (L10.3), erythematosus (L10.4), drug-induced pemphigus (L10.5) and other pemphigus (L10.8).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 595 (Major Skin Disorders with MCC, relative weight 2.0239) and DRG 596 (Major Skin Disorders without MCC, relative weight 1.1071), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.