ICD-10-CM 2027
ICD-10 code for nose congenital absence
From the official ICD-10-CM alphabetic index entry “Absence (of) (organ or part) (complete or partial) › nose (congenital)”. Page updated September 29, 2026.
About coding nose congenital absence
The ICD-10-CM code for nose congenital absence is Q30.1 (Agenesis and underdevelopment of nose). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q30.1.
Within Q30 (congenital malformations of nose), Q30.1 is specifically for agenesis and underdevelopment of nose. Related codes cover Choanal atresia (Q30.0), Fissured, notched and cleft nose (Q30.2), congenital perforated nasal septum (Q30.3), other congenital malformations of nose (Q30.8) and congenital malformation of nose, unspecified (Q30.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 154 (Other Ear, Nose, Mouth and Throat Diagnoses with MCC, relative weight 1.5921), DRG 155 (Other Ear, Nose, Mouth and Throat Diagnoses with CC, relative weight 0.9322) and DRG 156 (Other Ear, Nose, Mouth and Throat Diagnoses without CC/MCC, relative weight 0.6659), in MDC 03 (Diseases and Disorders of the Ear, Nose, Mouth and Throat), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific nose congenital absence codes (official index)
- acquired Z90.09 — Acquired absence of other part of head and neck
Common questions about nose congenital absence ICD-10 codes
What is the ICD-10 code for nose congenital absence?
- Q30.1 — Agenesis and underdevelopment of nose. More specific codes apply when the documentation supports them: Z90.09.
What is the ICD-10 code for acquired nose congenital absence?
- Z90.09 — Acquired absence of other part of head and neck.
Is Q30.1 billable?
- Yes. Q30.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q30.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q30.1 as a principal diagnosis.
Is Q30.1 a CC or MCC?
- No. Q30.1 is neither a CC nor an MCC under MS-DRG v44.0.