ICD-10-CM 2027
ICD-10 code for neurofibromatosis
From the official ICD-10-CM alphabetic index entry “Neurofibromatosis (multiple) (nonmalignant)”. Page updated September 29, 2026.
About coding neurofibromatosis
The ICD-10-CM code for neurofibromatosis is Q85.00 (Neurofibromatosis, unspecified). The official index lists 4 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q85.00.
Within Q85.0, choose Q85.00 (Neurofibromatosis, unspecified) only when documentation doesn't support a more specific option: neurofibromatosis, type 1 (Q85.01), neurofibromatosis, type 2 (Q85.02), Schwannomatosis (Q85.03) and other neurofibromatosis (Q85.09).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific neurofibromatosis codes (official index)
Common questions about neurofibromatosis ICD-10 codes
What is the ICD-10 code for neurofibromatosis?
- Q85.00 — Neurofibromatosis, unspecified. More specific codes apply when the documentation supports them: Q85.02, Q85.09, Q85.01, Q85.02.
What is the ICD-10 code for acoustic neurofibromatosis?
- Q85.02 — Neurofibromatosis, type 2.
What is the ICD-10 code for type 1 neurofibromatosis?
- Q85.01 — Neurofibromatosis, type 1.
What is the ICD-10 code for type 2 neurofibromatosis?
- Q85.02 — Neurofibromatosis, type 2.
Is Q85.00 billable?
- Yes. Q85.00 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q85.00 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q85.00 as a principal diagnosis.
Is Q85.00 a CC or MCC?
- No. Q85.00 is neither a CC nor an MCC under MS-DRG v44.0.