ICD-10-CM 2027
ICD-10 code for neonatal adrenoleukodystrophy
From the official ICD-10-CM alphabetic index entry “Adrenoleukodystrophy › neonatal”. Page updated September 29, 2026.
About coding neonatal adrenoleukodystrophy
The ICD-10-CM code for neonatal adrenoleukodystrophy is E71.511 (Neonatal adrenoleukodystrophy).
Within E71.51 (disorders of peroxisome biogenesis), E71.511 is specifically for neonatal adrenoleukodystrophy. Related codes cover Zellweger syndrome (E71.510) and other disorders of peroxisome biogenesis (E71.518).
Don't report E71.511 together with the conditions in its Excludes1 note: X-linked adrenoleukodystrophy (E71.42-).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for E71.511)
- X-linked adrenoleukodystrophy (E71.42-)
Common questions about neonatal adrenoleukodystrophy ICD-10 codes
What is the ICD-10 code for neonatal adrenoleukodystrophy?
- E71.511 — Neonatal adrenoleukodystrophy.
Is E71.511 billable?
- Yes. E71.511 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.511 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.511 as a principal diagnosis.
Is E71.511 a CC or MCC?
- E71.511 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.