ICD-10-CM 2027
ICD-10 code for Naegeli's disease
From the official ICD-10-CM alphabetic index entry “Disease, diseased › Naegeli's”. Page updated September 29, 2026.
About coding Naegeli's disease
The ICD-10-CM code for Naegeli's disease is Q82.8 (Other specified congenital malformations of skin). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q82.8.
Within Q82, choose Q82.8 (Other specified congenital malformations of skin) only when documentation doesn't support a more specific option: hereditary lymphedema (Q82.0), Xeroderma pigmentosum (Q82.1), congenital cutaneous mastocytosis (Q82.2), Incontinentia pigmenti (Q82.3), ectodermal dysplasia (anhidrotic) (Q82.4), congenital non-neoplastic nevus (Q82.5), congenital sacral dimple (Q82.6) and congenital malformation of skin, unspecified (Q82.9).
Don't report Q82.8 together with the conditions in its Excludes1 note: Ehlers-Danlos syndromes (Q79.6-).
The conditions in its Excludes2 note aren't part of Q82.8, but may be coded alongside it if the patient has both: disorders of pyrophosphate metabolism (E83.82-).
More specific Naegeli's disease codes (official index)
- meaning Glanzmann-Naegeli disease or thrombasthenia D69.11 — Glanzmann thrombasthenia
Don't confuse with (Excludes1 for Q82.8)
- Ehlers-Danlos syndromes (Q79.6-)
Common questions about Naegeli's disease ICD-10 codes
What is the ICD-10 code for Naegeli's disease?
- Q82.8 — Other specified congenital malformations of skin. More specific codes apply when the documentation supports them: D69.11.
Is Q82.8 billable?
- Yes. Q82.8 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q82.8 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q82.8 as a principal diagnosis.
Is Q82.8 a CC or MCC?
- No. Q82.8 is neither a CC nor an MCC under MS-DRG v44.0.