ICD-10 code for myotubular centronuclear myopathy

The ICD-10-CM code for myotubular centronuclear myopathy is G71.220 (X-linked myotubular myopathy). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on G71.220.

Within G71.22 (centronuclear myopathy), G71.220 is specifically for X-linked myotubular myopathy. Related codes cover other centronuclear myopathy (G71.228).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.