ICD-10 code for mitral valve atresia

The ICD-10-CM code for mitral valve atresia is Q23.2 (Congenital mitral stenosis). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q23.2.

Within Q23 (congenital malformations of aortic and mitral valves), Q23.2 is specifically for congenital mitral stenosis. Related codes cover congenital stenosis of aortic valve (Q23.0), congenital insufficiency of aortic valve (Q23.1), congenital mitral insufficiency (Q23.3), Hypoplastic left heart syndrome (Q23.4), other congenital malformations of aortic and mitral valves (Q23.8) and congenital malformation of aortic and mitral valves, unspecified (Q23.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.