ICD-10 code for Mandibulofacial dysostosis syndrome

The ICD-10-CM code for Mandibulofacial dysostosis syndrome is Q75.4 (Mandibulofacial dysostosis).

Within Q75 (other congenital malformations of skull and face bones), Q75.4 is specifically for Mandibulofacial dysostosis. Related codes cover craniosynostosis (Q75.0), craniofacial dysostosis (Q75.1), Hypertelorism (Q75.2), Macrocephaly (Q75.3), Oculomandibular dysostosis (Q75.5), other specified congenital malformations of skull and face bones (Q75.8) and congenital malformation of skull and face bones, unspecified (Q75.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.