Skip to content
Dx

ICD-10-CM 2027

ICD-10 code for malformation

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Malformation (congenital)”. Page updated September 29, 2026.

About coding malformation

The official ICD-10-CM index doesn't give a single default code for malformation; the code depends on the details below.

More specific malformation codes (official index)

  • adrenal gland Q89.1 — Congenital malformations of adrenal gland
  • affecting multiple systems with skeletal changes NEC Q87.5 — Other congenital malformation syndromes with other skeletal changes
  • alimentary tract Q45.9 — Congenital malformation of digestive system, unspecified
  • specified type NEC Q45.8 — Other specified congenital malformations of digestive system
  • upper Q40.9 — Congenital malformation of upper alimentary tract, unspecified
  • specified type NEC Q40.8 — Other specified congenital malformations of upper alimentary tract
  • aorta Q25.40 — Congenital malformation of aorta unspecified
  • absence Q25.41 — Absence and aplasia of aorta
  • aneurysm, congenital Q25.43 — Congenital aneurysm of aorta
  • aplasia Q25.41 — Absence and aplasia of aorta
  • atresia Q25.29 — Other atresia of aorta
  • aortic arch Q25.21 — Interruption of aortic arch
  • coarctation (preductal) (postductal) Q25.1 — Coarctation of aorta
  • dilatation, congenital Q25.44 — Congenital dilation of aorta
  • hypoplasia Q25.42 — Hypoplasia of aorta
  • patent ductus arteriosus Q25.0 — Patent ductus arteriosus
  • specified type NEC Q25.49 — Other congenital malformations of aorta
  • stenosis Q25.1 — Coarctation of aorta
  • supravalvular Q25.3 — Supravalvular aortic stenosis
  • aortic valve Q23.9 — Congenital malformation of aortic and mitral valves, unspecified
  • specified NEC Q23.88 — Other congenital malformations of aortic and mitral valves
  • arteriovenous, aneurysmatic (congenital) Q27.30 — Arteriovenous malformation, site unspecified
  • brain Q28.2 — Arteriovenous malformation of cerebral vessels
  • ruptured I60.8 — Other nontraumatic subarachnoid hemorrhage
  • intracerebral I61.8 — Other nontraumatic intracerebral hemorrhage
  • intraparenchymal I61.8 — Other nontraumatic intracerebral hemorrhage
  • intraventricular I61.5 — Nontraumatic intracerebral hemorrhage, intraventricular
  • subarachnoid I60.8 — Other nontraumatic subarachnoid hemorrhage
  • cerebral Q28.2 — Arteriovenous malformation of cerebral vessels
  • peripheral Q27.30 — Arteriovenous malformation, site unspecified
  • digestive system
  • congenital Q27.33 — Arteriovenous malformation of digestive system vessel
  • lower limb Q27.32 — Arteriovenous malformation of vessel of lower limb
  • other specified site Q27.39 — Arteriovenous malformation, other site
  • renal vessel Q27.34 — Arteriovenous malformation of renal vessel
  • upper limb Q27.31 — Arteriovenous malformation of vessel of upper limb
  • precerebral vessels (nonruptured) Q28.0 — Arteriovenous malformation of precerebral vessels
  • auricle
  • ear (congenital) Q17.3 — Other misshapen ear
  • acquired H61.119 — Acquired deformity of pinna, unspecified ear
  • left H61.112 — Acquired deformity of pinna, left ear
  • with right H61.113 — Acquired deformity of pinna, bilateral
  • right H61.111 — Acquired deformity of pinna, right ear
  • with left H61.113 — Acquired deformity of pinna, bilateral
  • bile duct Q44.5 — Other congenital malformations of bile ducts
  • bladder Q64.79 — Other congenital malformations of bladder and urethra
  • aplasia Q64.5 — Congenital absence of bladder and urethra
  • diverticulum Q64.6 — Congenital diverticulum of bladder
  • exstrophy
  • neck obstruction Q64.31 — Congenital bladder neck obstruction
  • bone Q79.9 — Congenital malformation of musculoskeletal system, unspecified
  • face Q75.9 — Congenital malformation of skull and face bones, unspecified
  • specified type NEC Q75.8 — Other specified congenital malformations of skull and face bones
  • skull Q75.9 — Congenital malformation of skull and face bones, unspecified
  • specified type NEC Q75.8 — Other specified congenital malformations of skull and face bones
  • brain (multiple) Q04.9 — Congenital malformation of brain, unspecified
  • arteriovenous Q28.2 — Arteriovenous malformation of cerebral vessels
  • specified type NEC Q04.8 — Other specified congenital malformations of brain
  • branchial cleft Q18.2 — Other branchial cleft malformations
  • breast Q83.9 — Congenital malformation of breast, unspecified
  • specified type NEC Q83.8 — Other congenital malformations of breast
  • broad ligament Q50.6 — Other congenital malformations of fallopian tube and broad ligament
  • bronchus Q32.4 — Other congenital malformations of bronchus
  • bursa Q79.9 — Congenital malformation of musculoskeletal system, unspecified
  • cardiac
  • chambers Q20.9 — Congenital malformation of cardiac chambers and connections, unspecified
  • specified type NEC Q20.8 — Other congenital malformations of cardiac chambers and connections
  • septum Q21.9 — Congenital malformation of cardiac septum, unspecified
  • specified type NEC Q21.8 — Other congenital malformations of cardiac septa
  • cerebral Q04.9 — Congenital malformation of brain, unspecified
  • vessels Q28.3 — Other malformations of cerebral vessels
  • cervix uteri Q51.9 — Congenital malformation of uterus and cervix, unspecified
  • specified type NEC Q51.828 — Other congenital malformations of cervix
  • Chiari
  • Type I G93.5 — Compression of brain
  • Type II Q07.01 — Arnold-Chiari syndrome with spina bifida
  • choroid (congenital) Q14.3 — Congenital malformation of choroid
  • plexus Q07.8 — Other specified congenital malformations of nervous system
  • circulatory system Q28.9 — Congenital malformation of circulatory system, unspecified
  • cochlea Q16.5 — Congenital malformation of inner ear
  • cornea Q13.4 — Other congenital corneal malformations
  • coronary vessels Q24.5 — Malformation of coronary vessels
  • corpus callosum (congenital) Q04.0 — Congenital malformations of corpus callosum
  • diaphragm Q79.1 — Other congenital malformations of diaphragm
  • digestive system NEC, specified type NEC Q45.8 — Other specified congenital malformations of digestive system
  • dura Q07.9 — Congenital malformation of nervous system, unspecified
  • brain Q04.9 — Congenital malformation of brain, unspecified
  • spinal Q06.9 — Congenital malformation of spinal cord, unspecified
  • ear Q17.9 — Congenital malformation of ear, unspecified
  • causing impairment of hearing Q16.9 — Congenital malformation of ear causing impairment of hearing, unspecified
  • external Q17.9 — Congenital malformation of ear, unspecified
  • accessory auricle Q17.0 — Accessory auricle
  • causing impairment of hearing Q16.9 — Congenital malformation of ear causing impairment of hearing, unspecified
  • absence of
  • auditory canal Q16.1 — Congenital absence, atresia and stricture of auditory canal (external)
  • auricle Q16.0 — Congenital absence of (ear) auricle
  • macrotia Q17.1 — Macrotia
  • microtia Q17.2 — Microtia
  • misplacement Q17.4 — Misplaced ear
  • misshapen NEC Q17.3 — Other misshapen ear
  • prominence Q17.5 — Prominent ear
  • specified type NEC Q17.8 — Other specified congenital malformations of ear
  • inner Q16.5 — Congenital malformation of inner ear
  • middle Q16.4 — Other congenital malformations of middle ear
  • absence of eustachian tube Q16.2 — Absence of eustachian tube
  • ossicles (fusion) Q16.3 — Congenital malformation of ear ossicles
  • ossicles Q16.3 — Congenital malformation of ear ossicles
  • specified type NEC Q17.8 — Other specified congenital malformations of ear
  • epididymis Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • esophagus Q39.9 — Congenital malformation of esophagus, unspecified
  • specified type NEC Q39.8 — Other congenital malformations of esophagus
  • eye Q15.9 — Congenital malformation of eye, unspecified
  • lid Q10.3 — Other congenital malformations of eyelid
  • specified NEC Q15.8 — Other specified congenital malformations of eye
  • fallopian tube Q50.6 — Other congenital malformations of fallopian tube and broad ligament
  • genital organ
  • great
  • artery Q25.9 — Congenital malformation of great arteries, unspecified
  • aorta
  • pulmonary artery
  • specified type NEC Q25.8 — Other congenital malformations of other great arteries
  • vein Q26.9 — Congenital malformation of great vein, unspecified
  • anomalous
  • portal venous connection Q26.5 — Anomalous portal venous connection
  • pulmonary venous connection Q26.4 — Anomalous pulmonary venous connection, unspecified
  • partial Q26.3 — Partial anomalous pulmonary venous connection
  • total Q26.2 — Total anomalous pulmonary venous connection
  • persistent left superior vena cava Q26.1 — Persistent left superior vena cava
  • portal vein-hepatic artery fistula Q26.6 — Portal vein-hepatic artery fistula
  • specified type NEC Q26.8 — Other congenital malformations of great veins
  • vena cava stenosis, congenital Q26.0 — Congenital stenosis of vena cava
  • gum Q38.6 — Other congenital malformations of mouth
  • hair Q84.2 — Other congenital malformations of hair
  • heart Q24.9 — Congenital malformation of heart, unspecified
  • specified type NEC Q24.8 — Other specified congenital malformations of heart
  • integument Q84.9 — Congenital malformation of integument, unspecified
  • specified type NEC Q84.8 — Other specified congenital malformations of integument
  • internal ear Q16.5 — Congenital malformation of inner ear
  • intestine Q43.9 — Congenital malformation of intestine, unspecified
  • specified type NEC Q43.8 — Other specified congenital malformations of intestine
  • iris Q13.2 — Other congenital malformations of iris
  • joint Q74.9 — Unspecified congenital malformation of limb(s)
  • ankle Q74.2 — Other congenital malformations of lower limb(s), including pelvic girdle
  • lumbosacral Q76.49 — Other congenital malformations of spine, not associated with scoliosis
  • sacroiliac Q74.2 — Other congenital malformations of lower limb(s), including pelvic girdle
  • specified type NEC Q74.8 — Other specified congenital malformations of limb(s)
  • kidney Q63.9 — Congenital malformation of kidney, unspecified
  • accessory Q63.0 — Accessory kidney
  • giant Q63.3 — Hyperplastic and giant kidney
  • horseshoe Q63.1 — Lobulated, fused and horseshoe kidney
  • hydronephrosis Q62.0 — Congenital hydronephrosis
  • malposition Q63.2 — Ectopic kidney
  • specified type NEC Q63.8 — Other specified congenital malformations of kidney
  • lacrimal apparatus Q10.6 — Other congenital malformations of lacrimal apparatus
  • lip Q38.0 — Congenital malformations of lips, not elsewhere classified
  • lingual Q38.3 — Other congenital malformations of tongue
  • liver Q44.70 — Other congenital malformation of liver, unspecified
  • lung Q33.9 — Congenital malformation of lung, unspecified
  • meninges or membrane (congenital) Q07.9 — Congenital malformation of nervous system, unspecified
  • cerebral Q04.8 — Other specified congenital malformations of brain
  • spinal (cord) Q06.9 — Congenital malformation of spinal cord, unspecified
  • middle ear Q16.4 — Other congenital malformations of middle ear
  • ossicles Q16.3 — Congenital malformation of ear ossicles
  • mitral valve Q23.9 — Congenital malformation of aortic and mitral valves, unspecified
  • specified NEC Q23.88 — Other congenital malformations of aortic and mitral valves
  • Mondini's (congenital) (malformation, cochlea) Q16.5 — Congenital malformation of inner ear
  • mouth (congenital) Q38.6 — Other congenital malformations of mouth
  • multiple types NEC Q89.7 — Multiple congenital malformations, not elsewhere classified
  • musculoskeletal system Q79.9 — Congenital malformation of musculoskeletal system, unspecified
  • myocardium Q24.8 — Other specified congenital malformations of heart
  • nail Q84.6 — Other congenital malformations of nails
  • nervous system (central) Q07.9 — Congenital malformation of nervous system, unspecified
  • nose Q30.9 — Congenital malformation of nose, unspecified
  • specified type NEC Q30.8 — Other congenital malformations of nose
  • optic disc Q14.2 — Congenital malformation of optic disc
  • orbit Q10.7 — Congenital malformation of orbit
  • ovary Q50.39 — Other congenital malformation of ovary
  • palate Q38.5 — Congenital malformations of palate, not elsewhere classified
  • parathyroid gland Q89.2 — Congenital malformations of other endocrine glands
  • pelvic organs or tissues NEC
  • in pregnancy or childbirth O34.8 — Maternal care for other abnormalities of pelvic organs
  • causing obstructed labor O65.5 — Obstructed labor due to abnormality of maternal pelvic organs
  • penis Q55.69 — Other congenital malformation of penis
  • aplasia Q55.5 — Congenital absence and aplasia of penis
  • curvature (lateral) Q55.61 — Curvature of penis (lateral)
  • hypoplasia Q55.62 — Hypoplasia of penis
  • pericardium Q24.8 — Other specified congenital malformations of heart
  • peripheral vascular system Q27.9 — Congenital malformation of peripheral vascular system, unspecified
  • specified type NEC Q27.8 — Other specified congenital malformations of peripheral vascular system
  • pharynx Q38.8 — Other congenital malformations of pharynx
  • precerebral vessels Q28.1 — Other malformations of precerebral vessels
  • prostate Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • pulmonary
  • arteriovenous Q25.72 — Congenital pulmonary arteriovenous malformation
  • artery Q25.9 — Congenital malformation of great arteries, unspecified
  • atresia Q25.5 — Atresia of pulmonary artery
  • specified type NEC Q25.79 — Other congenital malformations of pulmonary artery
  • stenosis Q25.6 — Stenosis of pulmonary artery
  • valve Q22.3 — Other congenital malformations of pulmonary valve
  • renal artery Q27.2 — Other congenital malformations of renal artery
  • respiratory system Q34.9 — Congenital malformation of respiratory system, unspecified
  • retina Q14.1 — Congenital malformation of retina
  • scrotum
  • seminal vesicles Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • sense organs NEC Q07.9 — Congenital malformation of nervous system, unspecified
  • skin Q82.9 — Congenital malformation of skin, unspecified
  • specified NEC Q89.89 — Other specified congenital malformations
  • spinal
  • cord Q06.9 — Congenital malformation of spinal cord, unspecified
  • nerve root Q07.8 — Other specified congenital malformations of nervous system
  • spine Q76.49 — Other congenital malformations of spine, not associated with scoliosis
  • kyphosis
  • lordosis
  • spleen Q89.09 — Congenital malformations of spleen
  • stomach Q40.3 — Congenital malformation of stomach, unspecified
  • specified type NEC Q40.2 — Other specified congenital malformations of stomach
  • teeth, tooth K00.9 — Disorder of tooth development, unspecified
  • tendon Q79.9 — Congenital malformation of musculoskeletal system, unspecified
  • testis and scrotum Q55.20 — Unspecified congenital malformations of testis and scrotum
  • aplasia Q55.0 — Absence and aplasia of testis
  • hypoplasia Q55.1 — Hypoplasia of testis and scrotum
  • polyorchism Q55.21 — Polyorchism
  • retractile testis Q55.22 — Retractile testis
  • scrotal transposition Q55.23 — Scrotal transposition
  • specified NEC Q55.29 — Other congenital malformations of testis and scrotum
  • throat Q38.8 — Other congenital malformations of pharynx
  • thorax, bony Q76.9 — Congenital malformation of bony thorax, unspecified
  • thyroid gland Q89.2 — Congenital malformations of other endocrine glands
  • tongue (congenital) Q38.3 — Other congenital malformations of tongue
  • hypertrophy Q38.2 — Macroglossia
  • tie Q38.1 — Ankyloglossia
  • trachea Q32.1 — Other congenital malformations of trachea
  • tricuspid valve Q22.9 — Congenital malformation of tricuspid valve, unspecified
  • specified type NEC Q22.8 — Other congenital malformations of tricuspid valve
  • umbilical cord NEC (complicating delivery) O69.89 — Labor and delivery complicated by other cord complications
  • umbilicus Q89.9 — Congenital malformation, unspecified
  • ureter Q62.8 — Other congenital malformations of ureter
  • agenesis Q62.4 — Agenesis of ureter
  • duplication Q62.5 — Duplication of ureter
  • malposition
  • obstructive defect
  • vesico-uretero-renal reflux Q62.7 — Congenital vesico-uretero-renal reflux
  • urethra Q64.79 — Other congenital malformations of bladder and urethra
  • aplasia Q64.5 — Congenital absence of bladder and urethra
  • duplication Q64.74 — Double urethra
  • posterior valves Q64.2 — Congenital posterior urethral valves
  • prolapse Q64.71 — Congenital prolapse of urethra
  • stricture Q64.32 — Congenital stricture of urethra
  • urinary system Q64.9 — Congenital malformation of urinary system, unspecified
  • uterus Q51.9 — Congenital malformation of uterus and cervix, unspecified
  • specified type NEC Q51.818 — Other congenital malformations of uterus
  • vagina Q52.4 — Other congenital malformations of vagina
  • vascular system, peripheral Q27.9 — Congenital malformation of peripheral vascular system, unspecified
  • vas deferens Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • atresia Q55.3 — Atresia of vas deferens
  • venous
  • vulva Q52.70 — Unspecified congenital malformations of vulva

Common questions about malformation ICD-10 codes

What is the ICD-10 code for adrenal gland malformation?

Q89.1 — Congenital malformations of adrenal gland.

What is the ICD-10 code for alimentary tract malformation?

Q45.9 — Congenital malformation of digestive system, unspecified.

What is the ICD-10 code for aorta malformation?

Q25.40 — Congenital malformation of aorta unspecified.

What is the ICD-10 code for aortic valve malformation?

Q23.9 — Congenital malformation of aortic and mitral valves, unspecified.

What is the ICD-10 code for bile duct malformation?

Q44.5 — Other congenital malformations of bile ducts.

What is the ICD-10 code for bladder malformation?

Q64.79 — Other congenital malformations of bladder and urethra.

What is the ICD-10 code for bone malformation?

Q79.9 — Congenital malformation of musculoskeletal system, unspecified.