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ICD-10-CM 2027

ICD-10 code for Macularis eruptiva perstans telangiectasia

D47.01

Cutaneous mastocytosis

✓ Billable / specificCC — complication/comorbidity

From the official ICD-10-CM alphabetic index entry “Telangiectasia, telangiectasis (verrucous) › macularis eruptiva perstans”. Page updated September 29, 2026.

About coding Macularis eruptiva perstans telangiectasia

The ICD-10-CM code for Macularis eruptiva perstans telangiectasia is D47.01 (Cutaneous mastocytosis).

Within D47.0 (mast cell neoplasms of uncertain behavior), D47.01 is specifically for cutaneous mastocytosis. Related codes cover systemic mastocytosis (D47.02) and other mast cell neoplasms of uncertain behavior (D47.09).

Don't report D47.01 together with the conditions in its Excludes1 note: congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2), congenital urticaria pigmentosa (Q82.2) and extracutaneous mastocytoma (D47.09).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

Don't confuse with (Excludes1 for D47.01)

  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)

Common questions about Macularis eruptiva perstans telangiectasia ICD-10 codes

What is the ICD-10 code for Macularis eruptiva perstans telangiectasia?

D47.01 — Cutaneous mastocytosis.

Is D47.01 billable?

Yes. D47.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can D47.01 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict D47.01 as a principal diagnosis.

Is D47.01 a CC or MCC?

D47.01 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.