ICD-10-CM 2027
ICD-10 code for Macroglossia
From the official ICD-10-CM alphabetic index entry “Macroglossia (congenital)”. Page updated September 29, 2026.
About coding Macroglossia
The ICD-10-CM code for Macroglossia is Q38.2 (Macroglossia). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q38.2.
Within Q38 (other congenital malformations of tongue, mouth and pharynx), Q38.2 is specifically for Macroglossia. Related codes cover congenital malformations of lips, not elsewhere classified (Q38.0), Ankyloglossia (Q38.1), other congenital malformations of tongue (Q38.3), congenital malformations of salivary glands and ducts (Q38.4), congenital malformations of palate, not elsewhere classified (Q38.5), other congenital malformations of mouth (Q38.6), congenital pharyngeal pouch (Q38.7) and other congenital malformations of pharynx (Q38.8).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 011 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with MCC, relative weight 5.6154), DRG 012 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with CC, relative weight 4.381), DRG 013 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy without CC/MCC, relative weight 2.7307), DRG 157 (Dental and Oral Diseases with MCC, relative weight 1.809), DRG 158 (Dental and Oral Diseases with CC, relative weight 0.9366) and DRG 159 (Dental and Oral Diseases without CC/MCC, relative weight 0.6893), in Pre-MDC and MDC 03 (Diseases and Disorders of the Ear, Nose, Mouth and Throat), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific Macroglossia codes (official index)
- acquired K14.8 — Other diseases of tongue
Common questions about Macroglossia ICD-10 codes
What is the ICD-10 code for Macroglossia?
- Q38.2 — Macroglossia. More specific codes apply when the documentation supports them: K14.8.
What is the ICD-10 code for acquired macroglossia?
- K14.8 — Other diseases of tongue.
Is Q38.2 billable?
- Yes. Q38.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q38.2 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q38.2 as a principal diagnosis.
Is Q38.2 a CC or MCC?
- No. Q38.2 is neither a CC nor an MCC under MS-DRG v44.0.