ICD-10 code for lung congenital deformity

The ICD-10-CM code for lung congenital deformity is Q33.9 (Congenital malformation of lung, unspecified). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q33.9.

Within Q33, choose Q33.9 (Congenital malformation of lung, unspecified) only when documentation doesn't support a more specific option: congenital cystic lung (Q33.0), accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), agenesis of lung (Q33.3), congenital bronchiectasis (Q33.4), ectopic tissue in lung (Q33.5), congenital hypoplasia and dysplasia of lung (Q33.6) and other congenital malformations of lung (Q33.8).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 205 (Other Respiratory System Diagnoses with MCC, relative weight 1.8244) and DRG 206 (Other Respiratory System Diagnoses without MCC, relative weight 0.9257), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.