ICD-10-CM 2027
ICD-10 code for Lignac disease or syndrome
From the official ICD-10-CM alphabetic index entry “Lignac (-de Toni) (-Fanconi) (-Debré) disease or syndrome”. Page updated September 29, 2026.
About coding Lignac disease or syndrome
The ICD-10-CM code for Lignac disease or syndrome is E72.09 (Other disorders of amino-acid transport). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on E72.09.
Within E72.0, choose E72.09 (Other disorders of amino-acid transport) only when documentation doesn't support a more specific option: unspecified (E72.00), Cystinuria (E72.01), Hartnup's disease (E72.02), Lowe's syndrome (E72.03) and Cystinosis (E72.04).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific Lignac disease or syndrome codes (official index)
- with cystinosis E72.04 — Cystinosis
Common questions about Lignac disease or syndrome ICD-10 codes
What is the ICD-10 code for Lignac disease or syndrome?
- E72.09 — Other disorders of amino-acid transport. More specific codes apply when the documentation supports them: E72.04.
Is E72.09 billable?
- Yes. E72.09 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E72.09 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E72.09 as a principal diagnosis.
Is E72.09 a CC or MCC?
- E72.09 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.