ICD-10 code for Kugelberg-Welander disease

The ICD-10-CM code for Kugelberg-Welander disease is G12.1 (Other inherited spinal muscular atrophy).

Within G12, choose G12.1 (Other inherited spinal muscular atrophy) only when documentation doesn't support a more specific option: infantile spinal muscular atrophy, type I [Werdnig-Hoffman] (G12.0), motor neuron disease (G12.2), other spinal muscular atrophies and related syndromes (G12.8) and spinal muscular atrophy, unspecified (G12.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 056 (Degenerative Nervous System Disorders with MCC, relative weight 2.2655) and DRG 057 (Degenerative Nervous System Disorders without MCC, relative weight 1.2838), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.