ICD-10-CM 2027
ICD-10 code for Kaznelson's syndrome
Constitutional (pure) red blood cell aplasia
From the official ICD-10-CM alphabetic index entry “Kaznelson's syndrome (congenital hypoplastic anemia)”. Page updated September 29, 2026.
About coding Kaznelson's syndrome
The ICD-10-CM code for Kaznelson's syndrome is D61.01 (Constitutional (pure) red blood cell aplasia).
Within D61.0 (constitutional aplastic anemia), D61.01 is specifically for constitutional (pure) red blood cell aplasia. Related codes cover Shwachman-Diamond syndrome (D61.02), Fanconi anemia (D61.03) and other constitutional aplastic anemia (D61.09).
Don't report D61.01 together with the conditions in its Excludes1 note: acquired red cell aplasia (D60.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for D61.01)
- acquired red cell aplasia (D60.9)
Common questions about Kaznelson's syndrome ICD-10 codes
What is the ICD-10 code for Kaznelson's syndrome?
- D61.01 — Constitutional (pure) red blood cell aplasia.
Is D61.01 billable?
- Yes. D61.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D61.01 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D61.01 as a principal diagnosis.
Is D61.01 a CC or MCC?
- D61.01 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.