ICD-10-CM 2027
ICD-10 code for Kawasaki's syndrome
From the official ICD-10-CM alphabetic index entry “Kawasaki's syndrome”. Page updated September 29, 2026.
About coding Kawasaki's syndrome
The ICD-10-CM code for Kawasaki's syndrome is M30.3 (Mucocutaneous lymph node syndrome [Kawasaki]).
Within M30 (polyarteritis nodosa and related conditions), M30.3 is specifically for mucocutaneous lymph node syndrome [Kawasaki]. Related codes cover polyarteritis nodosa (M30.0), polyarteritis with lung involvement [Churg-Strauss] (M30.1), juvenile polyarteritis (M30.2) and other conditions related to polyarteritis nodosa (M30.8).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 545 (Connective Tissue Disorders with MCC, relative weight 2.3892), DRG 546 (Connective Tissue Disorders with CC, relative weight 1.1745) and DRG 547 (Connective Tissue Disorders without CC/MCC, relative weight 0.7526), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Kawasaki's syndrome ICD-10 codes
What is the ICD-10 code for Kawasaki's syndrome?
- M30.3 — Mucocutaneous lymph node syndrome [Kawasaki].
Is M30.3 billable?
- Yes. M30.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can M30.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict M30.3 as a principal diagnosis.
Is M30.3 a CC or MCC?
- M30.3 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.