ICD-10-CM 2027
ICD-10 code for Ichthyosiforme congenitum bullous erythema
From the official ICD-10-CM alphabetic index entry “Erythema, erythematous (infectional) (inflammation) › ichthyosiforme congenitum bullous”. Page updated September 29, 2026.
About coding Ichthyosiforme congenitum bullous erythema
The ICD-10-CM code for Ichthyosiforme congenitum bullous erythema is Q80.3 (Congenital bullous ichthyosiform erythroderma).
Within Q80 (congenital ichthyosis), Q80.3 is specifically for congenital bullous ichthyosiform erythroderma. Related codes cover ichthyosis vulgaris (Q80.0), X-linked ichthyosis (Q80.1), lamellar ichthyosis (Q80.2), Harlequin fetus (Q80.4), other congenital ichthyosis (Q80.8) and unspecified (Q80.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728) and DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Ichthyosiforme congenitum bullous erythema ICD-10 codes
What is the ICD-10 code for Ichthyosiforme congenitum bullous erythema?
- Q80.3 — Congenital bullous ichthyosiform erythroderma.
Is Q80.3 billable?
- Yes. Q80.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q80.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q80.3 as a principal diagnosis.
Is Q80.3 a CC or MCC?
- No. Q80.3 is neither a CC nor an MCC under MS-DRG v44.0.