ICD-10 code for Hyperimmunoglobulin E IgE syndrome

The ICD-10-CM code for Hyperimmunoglobulin E IgE syndrome is D82.4 (Hyperimmunoglobulin E [IgE] syndrome).

Within D82 (immunodeficiency associated with other major defects), D82.4 is specifically for Hyperimmunoglobulin E [IgE] syndrome. Related codes cover Wiskott-Aldrich syndrome (D82.0), Di George's syndrome (D82.1), immunodeficiency with short-limbed stature (D82.2), immunodeficiency following hereditary defective response to Epstein-Barr virus (D82.3), immunodeficiency associated with other specified major defects (D82.8) and immunodeficiency associated with major defect, unspecified (D82.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 814 (Reticuloendothelial and Immunity Disorders with MCC, relative weight 2.0729), DRG 815 (Reticuloendothelial and Immunity Disorders with CC, relative weight 1.0444) and DRG 816 (Reticuloendothelial and Immunity Disorders without CC/MCC, relative weight 0.7381), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.