ICD-10-CM 2027
ICD-10 code for Hermansky-Pudlak syndrome
From the official ICD-10-CM alphabetic index entry “Hermansky-Pudlak syndrome”. Page updated September 29, 2026.
About coding Hermansky-Pudlak syndrome
The ICD-10-CM code for Hermansky-Pudlak syndrome is E70.331 (Hermansky-Pudlak syndrome).
Within E70.33 (albinism with hematologic abnormality), E70.331 is specifically for Hermansky-Pudlak syndrome. Related codes cover Chediak-Higashi syndrome (E70.330), other albinism with hematologic abnormality (E70.338) and unspecified (E70.339).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Hermansky-Pudlak syndrome ICD-10 codes
What is the ICD-10 code for Hermansky-Pudlak syndrome?
- E70.331 — Hermansky-Pudlak syndrome.
Is E70.331 billable?
- Yes. E70.331 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E70.331 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E70.331 as a principal diagnosis.
Is E70.331 a CC or MCC?
- E70.331 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.