ICD-10-CM 2027
ICD-10 code for hereditary thrombocytopenia
Congenital and hereditary thrombocytopenia purpura
From the official ICD-10-CM alphabetic index entry “Thrombocytopenia, thrombocytopenic › hereditary”. Page updated September 29, 2026.
About coding hereditary thrombocytopenia
The ICD-10-CM code for hereditary thrombocytopenia is D69.42 (Congenital and hereditary thrombocytopenia purpura).
Within D69.4 (other primary thrombocytopenia), D69.42 is specifically for congenital and hereditary thrombocytopenia purpura. Related codes cover Evans syndrome (D69.41) and other primary thrombocytopenia (D69.49).
Code first congential or hereditary disorder, such as: thrombocytopenia with absent radius (TAR syndrome) (Q87.2).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about hereditary thrombocytopenia ICD-10 codes
What is the ICD-10 code for hereditary thrombocytopenia?
- D69.42 — Congenital and hereditary thrombocytopenia purpura.
Is D69.42 billable?
- Yes. D69.42 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D69.42 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D69.42 as a principal diagnosis.
Is D69.42 a CC or MCC?
- D69.42 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.