ICD-10-CM 2027
ICD-10 code for Hepatopulmonary syndrome
From the official ICD-10-CM alphabetic index entry “Syndrome › hepatopulmonary”. Page updated September 29, 2026.
About coding Hepatopulmonary syndrome
The ICD-10-CM code for Hepatopulmonary syndrome is K76.81 (Hepatopulmonary syndrome).
Within K76.8 (other specified diseases of liver), K76.81 is specifically for Hepatopulmonary syndrome. Related codes cover hepatic encephalopathy (K76.82), intestinal failure-associated liver disease (K76.83) and other specified diseases of liver (K76.89).
Code first underlying liver disease, such as: alcoholic cirrhosis of liver (K70.3-) and cirrhosis of liver without mention of alcohol (K74.6-).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Common questions about Hepatopulmonary syndrome ICD-10 codes
What is the ICD-10 code for Hepatopulmonary syndrome?
- K76.81 — Hepatopulmonary syndrome.
Is K76.81 billable?
- Yes. K76.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can K76.81 be used as a principal diagnosis?
- No. It is not acceptable as the principal diagnosis for an inpatient stay; it may be reported as a secondary diagnosis.
Is K76.81 a CC or MCC?
- No. K76.81 is neither a CC nor an MCC under MS-DRG v44.0.