ICD-10-CM 2027
ICD-10 code for familial hypoparathyroidism
From the official ICD-10-CM alphabetic index entry “Hypoparathyroidism › familial”. Page updated September 29, 2026.
About coding familial hypoparathyroidism
The ICD-10-CM code for familial hypoparathyroidism is E20.89 (Other specified hypoparathyroidism). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on E20.89.
Within E20.8, choose E20.89 (Other specified hypoparathyroidism) only when documentation doesn't support a more specific option: hypoparathyroidism due to impaired parathyroid hormone secretion (E20.81).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 643 (Endocrine Disorders with MCC, relative weight 1.6139), DRG 644 (Endocrine Disorders with CC, relative weight 1.0044), DRG 645 (Endocrine Disorders without CC/MCC, relative weight 0.7459), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific familial hypoparathyroidism codes (official index)
- isolated E20.818 — Other specified hypoparathyroidism due to impaired parathyroid hormone secretion
Common questions about familial hypoparathyroidism ICD-10 codes
What is the ICD-10 code for familial hypoparathyroidism?
- E20.89 — Other specified hypoparathyroidism. More specific codes apply when the documentation supports them: E20.818.
What is the ICD-10 code for isolated familial hypoparathyroidism?
- E20.818 — Other specified hypoparathyroidism due to impaired parathyroid hormone secretion.
Is E20.89 billable?
- Yes. E20.89 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E20.89 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E20.89 as a principal diagnosis.
Is E20.89 a CC or MCC?
- No. E20.89 is neither a CC nor an MCC under MS-DRG v44.0.