ICD-10-CM 2027
ICD-10 code for Enzymatic congenital methemoglobinemia
From the official ICD-10-CM alphabetic index entry “Methemoglobinemia › enzymatic (congenital)”. Page updated September 29, 2026.
About coding Enzymatic congenital methemoglobinemia
The ICD-10-CM code for Enzymatic congenital methemoglobinemia is D74.0 (Congenital methemoglobinemia).
Within D74 (methemoglobinemia), D74.0 is specifically for congenital methemoglobinemia. Related codes cover other methemoglobinemias (D74.8) and unspecified (D74.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 811 (Red Blood Cell Disorders with MCC, relative weight 1.3988) and DRG 812 (Red Blood Cell Disorders without MCC, relative weight 0.9234), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Enzymatic congenital methemoglobinemia ICD-10 codes
What is the ICD-10 code for Enzymatic congenital methemoglobinemia?
- D74.0 — Congenital methemoglobinemia.
Is D74.0 billable?
- Yes. D74.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D74.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D74.0 as a principal diagnosis.
Is D74.0 a CC or MCC?
- D74.0 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.