ICD-10-CM 2027
ICD-10 code for encephalitis
Encephalitis and encephalomyelitis, unspecified
From the official ICD-10-CM alphabetic index entry “Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute)”. Page updated September 29, 2026.
About coding encephalitis
The ICD-10-CM code for encephalitis is G04.90 (Encephalitis and encephalomyelitis, unspecified). The official index lists 129 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on G04.90.
Within G04.9, choose G04.90 (Encephalitis and encephalomyelitis, unspecified) only when documentation doesn't support a more specific option: myelitis, unspecified (G04.91).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 023 (Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis with MCC or Antineoplastic Implant or Epilepsy with Neurostimulator, relative weight 5.7444), DRG 024 (Craniotomy with Major Device Implant or Acute Complex CNS Principal Diagnosis without MCC, relative weight 3.9708), DRG 097 (Non-Bacterial Infection of Nervous System Except Viral Meningitis with MCC, relative weight 3.8226), DRG 098 (Non-Bacterial Infection of Nervous System Except Viral Meningitis with CC, relative weight 2.2706), DRG 099 (Non-Bacterial Infection of Nervous System Except Viral Meningitis without CC/MCC, relative weight 1.5256), DRG 974 (HIV with Major Related Condition with MCC, relative weight 3.0506) and 2 more, in MDC 01 (Diseases and Disorders of the Nervous System) and MDC 25 (Human Immunodeficiency Virus Infections), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific encephalitis codes (official index)
- acute A86 — Unspecified viral encephalitis
- disseminated G04.00 — Acute disseminated encephalitis and encephalomyelitis, unspecified
- infectious G04.01 — Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM)
- noninfectious G04.81 — Other encephalitis and encephalomyelitis
- postimmunization (postvaccination) G04.02 — Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis
- postinfectious G04.01 — Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM)
- inclusion body A85.8 — Other specified viral encephalitis
- necrotizing hemorrhagic G04.30 — Acute necrotizing hemorrhagic encephalopathy, unspecified
- postimmunization G04.32 — Postimmunization acute necrotizing hemorrhagic encephalopathy
- postinfectious G04.31 — Postinfectious acute necrotizing hemorrhagic encephalopathy
- specified NEC G04.39 — Other acute necrotizing hemorrhagic encephalopathy
- arboviral, arbovirus NEC A85.2 — Arthropod-borne viral encephalitis, unspecified
- arthropod-borne NEC (viral) A85.2 — Arthropod-borne viral encephalitis, unspecified
- Australian A83.4 — Australian encephalitis
- California (virus) A83.5 — California encephalitis
- Central European (tick-borne) A84.1 — Central European tick-borne encephalitis
- Czechoslovakian A84.1 — Central European tick-borne encephalitis
- Dawson's (inclusion body) A81.1 — Subacute sclerosing panencephalitis
- diffuse sclerosing A81.1 — Subacute sclerosing panencephalitis
- disseminated, acute G04.00 — Acute disseminated encephalitis and encephalomyelitis, unspecified
- due to
- cat scratch disease A28.1 — Cat-scratch disease
- human immunodeficiency virus (HIV) disease B20 — Human immunodeficiency virus [HIV] disease
- malaria
- rickettsiosis
- smallpox inoculation G04.02 — Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis
- typhus
- Eastern equine A83.2 — Eastern equine encephalitis
- endemic (viral) A86 — Unspecified viral encephalitis
- epidemic NEC (viral) A86 — Unspecified viral encephalitis
- equine (acute) (infectious) (viral) A83.9 — Mosquito-borne viral encephalitis, unspecified
- Eastern A83.2 — Eastern equine encephalitis
- Venezuelan A92.2 — Venezuelan equine fever
- Western A83.1 — Western equine encephalitis
- Far Eastern (tick-borne) A84.0 — Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis]
- following vaccination or other immunization procedure G04.02 — Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis
- herpes zoster B02.0 — Zoster encephalitis
- herpesviral B00.4 — Herpesviral encephalitis
- due to herpesvirus 6 B10.01 — Human herpesvirus 6 encephalitis
- due to herpesvirus 7 B10.09 — Other human herpesvirus encephalitis
- specified NEC B10.09 — Other human herpesvirus encephalitis
- Ilheus (virus) A83.8 — Other mosquito-borne viral encephalitis
- inclusion body A81.1 — Subacute sclerosing panencephalitis
- in (due to)
- actinomycosis A42.82 — Actinomycotic encephalitis
- adenovirus A85.1 — Adenoviral encephalitis
- African trypanosomiasis B56.9 — African trypanosomiasis, unspecified
- Chagas' disease (chronic) B57.42 — Meningoencephalitis in Chagas' disease
- cytomegalovirus B25.8 — Other cytomegaloviral diseases
- enterovirus A85.0 — Enteroviral encephalitis
- herpes (simplex) virus B00.4 — Herpesviral encephalitis
- due to herpesvirus 6 B10.01 — Human herpesvirus 6 encephalitis
- due to herpesvirus 7 B10.09 — Other human herpesvirus encephalitis
- specified NEC B10.09 — Other human herpesvirus encephalitis
- infectious disease NEC B99 — Other and unspecified infectious diseases
- influenza
- listeriosis A32.12 — Listerial meningoencephalitis
- measles B05.0 — Measles complicated by encephalitis
- mumps B26.2 — Mumps encephalitis
- naegleriasis B60.2 — Naegleriasis
- parasitic disease NEC B89 — Unspecified parasitic disease
- poliovirus A80.9 — Acute poliomyelitis, unspecified
- rubella B06.01 — Rubella encephalitis
- syphilis
- congenital A50.42 — Late congenital syphilitic encephalitis
- late A52.14 — Late syphilitic encephalitis
- systemic lupus erythematosus M32.19 — Other organ or system involvement in systemic lupus erythematosus
- toxoplasmosis (acquired) B58.2 — Toxoplasma meningoencephalitis
- congenital P37.1 — Congenital toxoplasmosis
- tuberculosis A17.82 — Tuberculous meningoencephalitis
- zoster B02.0 — Zoster encephalitis
- infectious (acute) (virus) NEC A86 — Unspecified viral encephalitis
- Japanese (B type) A83.0 — Japanese encephalitis
- La Crosse A83.5 — California encephalitis
- lead
- lethargica (acute) (infectious) A85.8 — Other specified viral encephalitis
- louping ill A84.89 — Other tick-borne viral encephalitis
- lupus erythematosus, systemic M32.19 — Other organ or system involvement in systemic lupus erythematosus
- lymphatica A87.2 — Lymphocytic choriomeningitis
- Mengo A85.8 — Other specified viral encephalitis
- meningococcal A39.81 — Meningococcal encephalitis
- Murray Valley A83.4 — Australian encephalitis
- otitic NEC H66.40 — Suppurative otitis media, unspecified, unspecified ear
- parasitic NOS B71.9 — Cestode infection, unspecified
- periaxial G37.0 — Diffuse sclerosis of central nervous system
- periaxialis (concentrica) (diffuse) G37.5 — Concentric sclerosis [Balo] of central nervous system
- postchickenpox B01.11 — Varicella encephalitis and encephalomyelitis
- postexanthematous NEC B09 — Unspecified viral infection characterized by skin and mucous membrane lesions
- postimmunization G04.02 — Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis
- postinfectious NEC G04.01 — Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM)
- postmeasles B05.0 — Measles complicated by encephalitis
- postvaccinal G04.02 — Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis
- postvaricella B01.11 — Varicella encephalitis and encephalomyelitis
- postviral NEC A86 — Unspecified viral encephalitis
- Powassan A84.81 — Powassan virus disease
- Rasmussen G04.81 — Other encephalitis and encephalomyelitis
- Rio Bravo A85.8 — Other specified viral encephalitis
- Russian
- autumnal A83.0 — Japanese encephalitis
- spring-summer (taiga) A84.0 — Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis]
- saturnine
- specified NEC G04.81 — Other encephalitis and encephalomyelitis
- St. Louis A83.3 — St Louis encephalitis
- subacute sclerosing A81.1 — Subacute sclerosing panencephalitis
- summer A83.0 — Japanese encephalitis
- suppurative G04.81 — Other encephalitis and encephalomyelitis
- tick-borne A84.9 — Tick-borne viral encephalitis, unspecified
- Torula, torular (cryptococcal) B45.1 — Cerebral cryptococcosis
- toxic NEC G92.8 — Other toxic encephalopathy
- trichinosis B75 — Trichinellosis
- type
- B A83.0 — Japanese encephalitis
- C A83.3 — St Louis encephalitis
- van Bogaert's A81.1 — Subacute sclerosing panencephalitis
- Venezuelan equine A92.2 — Venezuelan equine fever
- Vienna A85.8 — Other specified viral encephalitis
- viral, virus A86 — Unspecified viral encephalitis
- arthropod-borne NEC A85.2 — Arthropod-borne viral encephalitis, unspecified
- mosquito-borne A83.9 — Mosquito-borne viral encephalitis, unspecified
- Australian X disease A83.4 — Australian encephalitis
- California virus A83.5 — California encephalitis
- Eastern equine A83.2 — Eastern equine encephalitis
- Japanese (B type) A83.0 — Japanese encephalitis
- Murray Valley A83.4 — Australian encephalitis
- specified NEC A83.8 — Other mosquito-borne viral encephalitis
- St. Louis A83.3 — St Louis encephalitis
- type B A83.0 — Japanese encephalitis
- type C A83.3 — St Louis encephalitis
- Western equine A83.1 — Western equine encephalitis
- tick-borne A84.9 — Tick-borne viral encephalitis, unspecified
- biundulant A84.1 — Central European tick-borne encephalitis
- central European A84.1 — Central European tick-borne encephalitis
- Czechoslovakian A84.1 — Central European tick-borne encephalitis
- diphasic meningoencephalitis A84.1 — Central European tick-borne encephalitis
- Far Eastern A84.0 — Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis]
- Russian spring-summer (taiga) A84.0 — Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis]
- specified NEC A84.89 — Other tick-borne viral encephalitis
- specified type NEC A85.8 — Other specified viral encephalitis
- tick-borne, specified NEC A84.89 — Other tick-borne viral encephalitis
- Western equine A83.1 — Western equine encephalitis
Common questions about encephalitis ICD-10 codes
What is the ICD-10 code for encephalitis?
- G04.90 — Encephalitis and encephalomyelitis, unspecified. More specific codes apply when the documentation supports them: A86, G04.00, G04.01, G04.81 and others below.
What is the ICD-10 code for acute encephalitis?
- A86 — Unspecified viral encephalitis.
What is the ICD-10 code for arthropod-borne nec encephalitis?
- A85.2 — Arthropod-borne viral encephalitis, unspecified.
What is the ICD-10 code for australian encephalitis?
- A83.4 — Australian encephalitis.
What is the ICD-10 code for california encephalitis?
- A83.5 — California encephalitis.
What is the ICD-10 code for central european encephalitis?
- A84.1 — Central European tick-borne encephalitis.
What is the ICD-10 code for czechoslovakian encephalitis?
- A84.1 — Central European tick-borne encephalitis.
Is G04.90 billable?
- Yes. G04.90 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G04.90 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G04.90 as a principal diagnosis.
Is G04.90 a CC or MCC?
- G04.90 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.