ICD-10-CM 2027
ICD-10 code for dyserythropoietic congenital anemia
From the official ICD-10-CM alphabetic index entry “Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › dyserythropoietic (congenital)”. Page updated September 29, 2026.
About coding dyserythropoietic congenital anemia
The ICD-10-CM code for dyserythropoietic congenital anemia is D64.4 (Congenital dyserythropoietic anemia).
Within D64 (other anemias), D64.4 is specifically for congenital dyserythropoietic anemia. Related codes cover hereditary sideroblastic anemia (D64.0), secondary sideroblastic anemia due to disease (D64.1), secondary sideroblastic anemia due to drugs and toxins (D64.2), other sideroblastic anemias (D64.3), other specified anemias (D64.8) and anemia, unspecified (D64.9).
Don't report D64.4 together with the conditions in its Excludes1 note: Blackfan-Diamond syndrome (D61.01) and Di Guglielmo's disease (C94.0).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Don't confuse with (Excludes1 for D64.4)
Common questions about dyserythropoietic congenital anemia ICD-10 codes
What is the ICD-10 code for dyserythropoietic congenital anemia?
- D64.4 — Congenital dyserythropoietic anemia.
Is D64.4 billable?
- Yes. D64.4 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D64.4 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D64.4 as a principal diagnosis.
Is D64.4 a CC or MCC?
- No. D64.4 is neither a CC nor an MCC under MS-DRG v44.0.