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ICD-10-CM 2027

ICD-10 code for defect

Q89.9

Congenital malformation, unspecified

✓ Billable / specific

From the official ICD-10-CM alphabetic index entry “Defect, defective”. Page updated September 29, 2026.

About coding defect

The ICD-10-CM code for defect is Q89.9 (Congenital malformation, unspecified). The official index lists 220 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q89.9.

Within Q89, choose Q89.9 (Congenital malformation, unspecified) only when documentation doesn't support a more specific option: congenital absence and malformations of spleen (Q89.0), congenital malformations of adrenal gland (Q89.1), congenital malformations of other endocrine glands (Q89.2), Situs inversus (Q89.3), conjoined twins (Q89.4), multiple congenital malformations, not elsewhere classified (Q89.7) and other specified congenital malformations (Q89.8).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 951 (Other Factors Influencing Health Status, relative weight 0.5577), in MDC 23 (Factors Influencing Health Status and Other Contacts with Health Services), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

More specific defect codes (official index)

  • 3-beta-hydroxysteroid dehydrogenase E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency
  • 11-hydroxylase E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency
  • 21-hydroxylase E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency
  • abdominal wall, congenital Q79.59 — Other congenital malformations of abdominal wall
  • antibody immunodeficiency D80.9 — Immunodeficiency with predominantly antibody defects, unspecified
  • aorticopulmonary septum Q21.4 — Aortopulmonary septal defect
  • atrial septal Q21.10 — Atrial septal defect, unspecified
  • coronary sinus Q21.13 — Coronary sinus atrial septal defect
  • following acute myocardial infarction (current complication) I23.1 — Atrial septal defect as current complication following acute myocardial infarction
  • ostium primum type (type I) Q21.20 — Atrioventricular septal defect, unspecified as to partial or complete
  • with
  • common atrioventricular valves and moderate or larger inlet VSD Q21.23 — Complete atrioventricular septal defect
  • separate atrioventricular valves Q21.21 — Partial atrioventricular septal defect
  • and small or restrictive inlet VSD Q21.22 — Transitional atrioventricular septal defect
  • ostium secundum type (patent persistent) (type II) Q21.11 — Secundum atrial septal defect
  • sinus venosus Q21.16 — Sinus venosus atrial septal defect, unspecified
  • inferior Q21.15 — Inferior sinus venosus atrial septal defect
  • superior Q21.14 — Superior sinus venosus atrial septal defect
  • specified NEC Q21.19 — Other specified atrial septal defect
  • vena cava type
  • inferior Q21.15 — Inferior sinus venosus atrial septal defect
  • superior Q21.14 — Superior sinus venosus atrial septal defect
  • atrioventricular
  • canal Q21.20 — Atrioventricular septal defect, unspecified as to partial or complete
  • septal
  • common Q21.23 — Complete atrioventricular septal defect
  • complete Q21.23 — Complete atrioventricular septal defect
  • incomplete Q21.21 — Partial atrioventricular septal defect
  • intermediate Q21.22 — Transitional atrioventricular septal defect
  • partial Q21.21 — Partial atrioventricular septal defect
  • transitional Q21.22 — Transitional atrioventricular septal defect
  • unspecified as to partial or complete Q21.20 — Atrioventricular septal defect, unspecified as to partial or complete
  • septum Q21.20 — Atrioventricular septal defect, unspecified as to partial or complete
  • auricular septal Q21.10 — Atrial septal defect, unspecified
  • bilirubin excretion NEC E80.6 — Other disorders of bilirubin metabolism
  • biosynthesis, androgen (testicular) E29.1 — Testicular hypofunction
  • bulbar septum Q21.0 — Ventricular septal defect
  • catalase E80.3 — Defects of catalase and peroxidase
  • cell membrane receptor complex (CR3) D71.8 — Other functional disorders of polymorphonuclear neutrophils
  • circulation I99.9 — Unspecified disorder of circulatory system
  • congenital Q28.9 — Congenital malformation of circulatory system, unspecified
  • newborn Q28.9 — Congenital malformation of circulatory system, unspecified
  • coagulation (factor) D68.9 — Coagulation defect, unspecified
  • with
  • COVID-19 associated coagulopathy D68.8 — Other specified coagulation defects
  • ectopic pregnancy O08.1 — Delayed or excessive hemorrhage following ectopic and molar pregnancy
  • molar pregnancy O08.1 — Delayed or excessive hemorrhage following ectopic and molar pregnancy
  • acquired D68.4 — Acquired coagulation factor deficiency
  • antepartum with hemorrhage
  • due to
  • liver disease D68.4 — Acquired coagulation factor deficiency
  • vitamin K deficiency D68.4 — Acquired coagulation factor deficiency
  • hereditary NEC D68.2 — Hereditary deficiency of other clotting factors
  • intrapartum O67.0 — Intrapartum hemorrhage with coagulation defect
  • newborn, transient P61.6 — Other transient neonatal disorders of coagulation
  • postpartum O99.13 — Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating the puerperium
  • with hemorrhage O72.3 — Postpartum coagulation defects
  • specified type NEC D68.8 — Other specified coagulation defects
  • complement system D84.1 — Defects in the complement system
  • conduction (heart) I45.9 — Conduction disorder, unspecified
  • bone
  • congenital, organ or site not listed
  • coronary sinus Q21.13 — Coronary sinus atrial septal defect
  • cushion, endocardial Q21.20 — Atrioventricular septal defect, unspecified as to partial or complete
  • common Q21.23 — Complete atrioventricular septal defect
  • incomplete Q21.21 — Partial atrioventricular septal defect
  • intermediate Q21.22 — Transitional atrioventricular septal defect
  • transitional Q21.22 — Transitional atrioventricular septal defect
  • degradation, glycoprotein E77.1 — Defects in glycoprotein degradation
  • dental bridge, crown, fillings
  • dental restoration K08.50 — Unsatisfactory restoration of tooth, unspecified
  • specified NEC K08.59 — Other unsatisfactory restoration of tooth
  • dentin (hereditary) K00.5 — Hereditary disturbances in tooth structure, not elsewhere classified
  • Descemet's membrane, congenital Q13.89 — Other congenital malformations of anterior segment of eye
  • developmental
  • cauda equina Q06.3 — Other congenital cauda equina malformations
  • diaphragm
  • with elevation, eventration or hernia
  • congenital Q79.1 — Other congenital malformations of diaphragm
  • with hernia Q79.0 — Congenital diaphragmatic hernia
  • gross (with hernia) Q79.0 — Congenital diaphragmatic hernia
  • ectodermal, congenital Q82.9 — Congenital malformation of skin, unspecified
  • Eisenmenger's Q21.8 — Other congenital malformations of cardiac septa
  • enzyme
  • catalase E80.3 — Defects of catalase and peroxidase
  • peroxidase E80.3 — Defects of catalase and peroxidase
  • esophagus, congenital Q39.9 — Congenital malformation of esophagus, unspecified
  • extensor retinaculum M62.89 — Other specified disorders of muscle
  • fibrin polymerization D68.2 — Hereditary deficiency of other clotting factors
  • filling
  • bladder R93.41 — Abnormal radiologic findings on diagnostic imaging of renal pelvis, ureter, or bladder
  • kidney R93.42 — Abnormal radiologic findings on diagnostic imaging of kidney
  • renal pelvis R93.41 — Abnormal radiologic findings on diagnostic imaging of renal pelvis, ureter, or bladder
  • stomach R93.3 — Abnormal findings on diagnostic imaging of other parts of digestive tract
  • ureter R93.41 — Abnormal radiologic findings on diagnostic imaging of renal pelvis, ureter, or bladder
  • urinary organs, specified NEC R93.49 — Abnormal radiologic findings on diagnostic imaging of other urinary organs
  • GABA (gamma aminobutyric acid) metabolic E72.81 — Disorders of gamma aminobutyric acid metabolism
  • Gerbode Q21.0 — Ventricular septal defect
  • glucose transport, blood-brain barrier E74.810 — Glucose transporter protein type 1 deficiency
  • glycoprotein degradation E77.1 — Defects in glycoprotein degradation
  • Hageman (factor) D68.2 — Hereditary deficiency of other clotting factors
  • hearing
  • high grade F70 — Mild intellectual disabilities
  • home, technical, preventing adequate care Z59.19 — Other inadequate housing
  • interatrial septal Q21.19 — Other specified atrial septal defect
  • interauricular septal Q21.19 — Other specified atrial septal defect
  • interventricular septal Q21.0 — Ventricular septal defect
  • with dextroposition of aorta, pulmonary stenosis and hypertrophy of right ventricle Q21.3 — Tetralogy of Fallot
  • in tetralogy of Fallot Q21.3 — Tetralogy of Fallot
  • intervertebral annular fibrosis M51.9 — Unspecified thoracic, thoracolumbar and lumbosacral intervertebral disc disorder
  • lumbar M51.A0 — Intervertebral annulus fibrosus defect, lumbar region, unspecified size
  • large M51.A2 — Intervertebral annulus fibrosus defect, large, lumbar region
  • small M51.A1 — Intervertebral annulus fibrosus defect, small, lumbar region
  • lumbosacral M51.A3 — Intervertebral annulus fibrosus defect, lumbosacral region, unspecified size
  • large M51.A5 — Intervertebral annulus fibrosus defect, large, lumbosacral region
  • small M51.A4 — Intervertebral annulus fibrosus defect, small, lumbosacral region
  • learning (specific)
  • lymphocyte function antigen-1 (LFA-1) D84.0 — Lymphocyte function antigen-1 [LFA-1] defect
  • lysosomal enzyme, post-translational modification E77.0 — Defects in post-translational modification of lysosomal enzymes
  • major osseous M89.70 — Major osseous defect, unspecified site
  • ankle M89.77 — Major osseous defect, ankle and foot
  • carpus M89.74 — Major osseous defect, hand
  • clavicle M89.71 — Major osseous defect, shoulder region
  • femur M89.75 — Major osseous defect, pelvic region and thigh
  • fibula M89.76 — Major osseous defect, lower leg
  • fingers M89.74 — Major osseous defect, hand
  • foot M89.77 — Major osseous defect, ankle and foot
  • forearm M89.73 — Major osseous defect, forearm
  • hand M89.74 — Major osseous defect, hand
  • humerus M89.72 — Major osseous defect, humerus
  • lower leg M89.76 — Major osseous defect, lower leg
  • metacarpus M89.74 — Major osseous defect, hand
  • metatarsus M89.77 — Major osseous defect, ankle and foot
  • multiple sites M89.79 — Major osseous defect, multiple sites
  • pelvic region M89.75 — Major osseous defect, pelvic region and thigh
  • pelvis M89.75 — Major osseous defect, pelvic region and thigh
  • radius M89.73 — Major osseous defect, forearm
  • scapula M89.71 — Major osseous defect, shoulder region
  • shoulder region M89.71 — Major osseous defect, shoulder region
  • specified NEC M89.78 — Major osseous defect, other site
  • tarsus M89.77 — Major osseous defect, ankle and foot
  • thigh M89.75 — Major osseous defect, pelvic region and thigh
  • tibia M89.76 — Major osseous defect, lower leg
  • toes M89.77 — Major osseous defect, ankle and foot
  • ulna M89.73 — Major osseous defect, forearm
  • mental
  • modification, lysosomal enzymes, post-translational E77.0 — Defects in post-translational modification of lysosomal enzymes
  • obstructive, congenital
  • renal pelvis Q62.39 — Other obstructive defects of renal pelvis and ureter
  • ureter Q62.39 — Other obstructive defects of renal pelvis and ureter
  • atresia
  • cecoureterocele Q62.32 — Cecoureterocele
  • megaureter Q62.2 — Congenital megaureter
  • orthotopic ureterocele Q62.31 — Congenital ureterocele, orthotopic
  • osseous, major M89.70 — Major osseous defect, unspecified site
  • ankle M89.77 — Major osseous defect, ankle and foot
  • carpus M89.74 — Major osseous defect, hand
  • clavicle M89.71 — Major osseous defect, shoulder region
  • femur M89.75 — Major osseous defect, pelvic region and thigh
  • fibula M89.76 — Major osseous defect, lower leg
  • fingers M89.74 — Major osseous defect, hand
  • foot M89.77 — Major osseous defect, ankle and foot
  • forearm M89.73 — Major osseous defect, forearm
  • hand M89.74 — Major osseous defect, hand
  • humerus M89.72 — Major osseous defect, humerus
  • lower leg M89.76 — Major osseous defect, lower leg
  • metacarpus M89.74 — Major osseous defect, hand
  • metatarsus M89.77 — Major osseous defect, ankle and foot
  • multiple sites M89.9 — Disorder of bone, unspecified
  • pelvic region M89.75 — Major osseous defect, pelvic region and thigh
  • pelvis M89.75 — Major osseous defect, pelvic region and thigh
  • radius M89.73 — Major osseous defect, forearm
  • scapula M89.71 — Major osseous defect, shoulder region
  • shoulder region M89.71 — Major osseous defect, shoulder region
  • specified NEC M89.78 — Major osseous defect, other site
  • tarsus M89.77 — Major osseous defect, ankle and foot
  • thigh M89.75 — Major osseous defect, pelvic region and thigh
  • tibia M89.76 — Major osseous defect, lower leg
  • toes M89.77 — Major osseous defect, ankle and foot
  • ulna M89.73 — Major osseous defect, forearm
  • osteochondral NEC M95.8 — Other specified acquired deformities of musculoskeletal system
  • ostium
  • primum Q21.20 — Atrioventricular septal defect, unspecified as to partial or complete
  • secundum Q21.11 — Secundum atrial septal defect
  • peroxidase E80.3 — Defects of catalase and peroxidase
  • placental blood supply
  • platelets, qualitative D69.19 — Other qualitative platelet defects
  • constitutional
  • postural NEC, spine
  • qualitative, of von Willebrand factor
  • with
  • decreased platelet adhesion and selective deficiency of high-molecular-weight multimers D68.020 — Von Willebrand disease, type 2A
  • defective platelet adhesion with a normal size distribution of von Willebrand factor multimers D68.022 — Von Willebrand disease, type 2M
  • defective von Willebrand factor to factor VIII binding D68.023 — Von Willebrand disease, type 2N
  • high-molecular-weight von Willebrand factor loss D68.021 — Von Willebrand disease, type 2B
  • hyper-adhesive forms D68.021 — Von Willebrand disease, type 2B
  • increased affinity for platelet glycoprotein lb D68.021 — Von Willebrand disease, type 2B
  • markedly decreased affinity for factor VIII D68.023 — Von Willebrand disease, type 2N
  • in von Willebrand factor function, with no further subtyping D68.029 — Von Willebrand disease, type 2, unspecified
  • reduction
  • limb Q73.8 — Other reduction defects of unspecified limb(s)
  • lower Q72.9 — Unspecified reduction defect of lower limb
  • absence
  • foot
  • longitudinal
  • femur Q72.4 — Longitudinal reduction defect of femur
  • fibula Q72.6 — Longitudinal reduction defect of fibula
  • tibia Q72.5 — Longitudinal reduction defect of tibia
  • specified type NEC Q72.89 — Other reduction defects of lower limb
  • split foot Q72.7 — Split foot
  • specified type NEC Q73.8 — Other reduction defects of unspecified limb(s)
  • upper Q71.9 — Unspecified reduction defect of upper limb
  • absence
  • forearm
  • hand
  • lobster-claw hand Q71.6 — Lobster-claw hand
  • longitudinal
  • radius Q71.4 — Longitudinal reduction defect of radius
  • ulna Q71.5 — Longitudinal reduction defect of ulna
  • specified type NEC Q71.89 — Other reduction defects of upper limb
  • renal pelvis Q63.8 — Other specified congenital malformations of kidney
  • obstructive Q62.39 — Other obstructive defects of renal pelvis and ureter
  • respiratory system, congenital Q34.9 — Congenital malformation of respiratory system, unspecified
  • restoration, dental K08.50 — Unsatisfactory restoration of tooth, unspecified
  • specified NEC K08.59 — Other unsatisfactory restoration of tooth
  • retinal nerve bundle fibers H35.89 — Other specified retinal disorders
  • septal (heart) NOS Q21.9 — Congenital malformation of cardiac septum, unspecified
  • acquired (atrial) (auricular) (ventricular) (old) I51.0 — Cardiac septal defect, acquired
  • atrial Q21.10 — Atrial septal defect, unspecified
  • concurrent with acute myocardial infarction
  • following acute myocardial infarction (current complication) I23.1 — Atrial septal defect as current complication following acute myocardial infarction
  • ventricular Q21.0 — Ventricular septal defect
  • sinus venosus Q21.16 — Sinus venosus atrial septal defect, unspecified
  • speech
  • developmental F80.9 — Developmental disorder of speech and language, unspecified
  • specified NEC R47.89 — Other speech disturbances
  • Taussig-Bing (aortic transposition and overriding pulmonary artery) Q20.1 — Double outlet right ventricle
  • teeth, wedge K03.1 — Abrasion of teeth
  • vascular (local) I99.9 — Unspecified disorder of circulatory system
  • congenital Q27.9 — Congenital malformation of peripheral vascular system, unspecified
  • ventricular septal Q21.0 — Ventricular septal defect
  • concurrent with acute myocardial infarction
  • following acute myocardial infarction (current complication) I23.2 — Ventricular septal defect as current complication following acute myocardial infarction
  • in tetralogy of Fallot Q21.3 — Tetralogy of Fallot
  • vision NEC H54.7 — Unspecified visual loss
  • visual field H53.40 — Unspecified visual field defects
  • bilateral
  • heteronymous H53.47 — Heteronymous bilateral field defects
  • homonymous H53.46 — Homonymous bilateral field defects
  • generalized contraction H53.48 — Generalized contraction of visual field
  • localized
  • arcuate H53.43 — Sector or arcuate defects
  • scotoma (central area) H53.41 — Scotoma involving central area
  • blind spot area H53.42 — Scotoma of blind spot area
  • sector H53.43 — Sector or arcuate defects
  • specified type NEC H53.45 — Other localized visual field defect
  • voice R49.9 — Unspecified voice and resonance disorder
  • specified NEC R49.8 — Other voice and resonance disorders
  • wedge, tooth, teeth (abrasion) K03.1 — Abrasion of teeth

Common questions about defect ICD-10 codes

What is the ICD-10 code for defect?

Q89.9 — Congenital malformation, unspecified. More specific codes apply when the documentation supports them: E25.0, E25.0, E25.0, Q79.59 and others below.

What is the ICD-10 code for 3-beta-hydroxysteroid dehydrogenase defect?

E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency.

What is the ICD-10 code for 11-hydroxylase defect?

E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency.

What is the ICD-10 code for 21-hydroxylase defect?

E25.0 — Congenital adrenogenital disorders associated with enzyme deficiency.

What is the ICD-10 code for antibody immunodeficiency defect?

D80.9 — Immunodeficiency with predominantly antibody defects, unspecified.

What is the ICD-10 code for aorticopulmonary septum defect?

Q21.4 — Aortopulmonary septal defect.

What is the ICD-10 code for atrial septal defect?

Q21.10 — Atrial septal defect, unspecified.

Is Q89.9 billable?

Yes. Q89.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q89.9 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q89.9 as a principal diagnosis.

Is Q89.9 a CC or MCC?

No. Q89.9 is neither a CC nor an MCC under MS-DRG v44.0.