ICD-10-CM 2027
ICD-10 code for connection anomaly
Choose a code from the options below based on the documentation.
From the official ICD-10-CM alphabetic index entry “Anomaly, anomalous (congenital) (unspecified type) › connection”. Page updated September 29, 2026.
About coding connection anomaly
The official ICD-10-CM index doesn't give a single default code for connection anomaly; the code depends on the details below.
More specific connection anomaly codes (official index)
- portal vein Q26.5 — Anomalous portal venous connection
- pulmonary venous Q26.4 — Anomalous pulmonary venous connection, unspecified
- partial Q26.3 — Partial anomalous pulmonary venous connection
- total Q26.2 — Total anomalous pulmonary venous connection
- renal artery with kidney Q27.2 — Other congenital malformations of renal artery
Common questions about connection anomaly ICD-10 codes
What is the ICD-10 code for portal vein connection anomaly?
- Q26.5 — Anomalous portal venous connection.
What is the ICD-10 code for pulmonary venous connection anomaly?
- Q26.4 — Anomalous pulmonary venous connection, unspecified.
What is the ICD-10 code for renal artery with kidney connection anomaly?
- Q27.2 — Other congenital malformations of renal artery.