ICD-10-CM 2027
ICD-10 code for congenital nontoxic goiter
From the official ICD-10-CM alphabetic index entry “Goiter (plunging) (substernal) › congenital (nontoxic)”. Page updated September 29, 2026.
About coding congenital nontoxic goiter
The ICD-10-CM code for congenital nontoxic goiter is E03.0 (Congenital hypothyroidism with diffuse goiter). The official index lists 3 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on E03.0.
Within E03 (other hypothyroidism), E03.0 is specifically for congenital hypothyroidism with diffuse goiter. Related codes cover congenital hypothyroidism without goiter (E03.1), hypothyroidism due to medicaments and other exogenous substances (E03.2), postinfectious hypothyroidism (E03.3), atrophy of thyroid (acquired) (E03.4), myxedema coma (E03.5), other specified hypothyroidism (E03.8) and hypothyroidism, unspecified (E03.9).
Don't report E03.0 together with the conditions in its Excludes1 note: transitory congenital goiter with normal function (P72.0).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
More specific congenital nontoxic goiter codes (official index)
Don't confuse with (Excludes1 for E03.0)
- transitory congenital goiter with normal function (P72.0)
Common questions about congenital nontoxic goiter ICD-10 codes
What is the ICD-10 code for congenital nontoxic goiter?
- E03.0 — Congenital hypothyroidism with diffuse goiter. More specific codes apply when the documentation supports them: E03.0, E03.0, P72.0.
What is the ICD-10 code for diffuse congenital nontoxic goiter?
- E03.0 — Congenital hypothyroidism with diffuse goiter.
What is the ICD-10 code for parenchymatous congenital nontoxic goiter?
- E03.0 — Congenital hypothyroidism with diffuse goiter.
Is E03.0 billable?
- Yes. E03.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E03.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E03.0 as a principal diagnosis.
Is E03.0 a CC or MCC?
- No. E03.0 is neither a CC nor an MCC under MS-DRG v44.0.