ICD-10-CM 2027
ICD-10 code for congenital nonprogressive ataxia
From the official ICD-10-CM alphabetic index entry “Ataxia, ataxy, ataxic › congenital nonprogressive”. Page updated September 29, 2026.
About coding congenital nonprogressive ataxia
The ICD-10-CM code for congenital nonprogressive ataxia is G11.0 (Congenital nonprogressive ataxia).
Within G11 (hereditary ataxia), G11.0 is specifically for congenital nonprogressive ataxia. Related codes cover early-onset cerebellar ataxia (G11.1), Late-onset cerebellar ataxia (G11.2), cerebellar ataxia with defective DNA repair (G11.3), hereditary spastic paraplegia (G11.4), Hypomyelination - hypogonadotropic hypogonadism - hypodontia (G11.5), leukodystrophy with vanishing white matter disease (G11.6), other hereditary ataxias (G11.8) and unspecified (G11.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC, relative weight 1.8438), DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC, relative weight 1.2002) and DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC, relative weight 0.9247), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about congenital nonprogressive ataxia ICD-10 codes
What is the ICD-10 code for congenital nonprogressive ataxia?
- G11.0 — Congenital nonprogressive ataxia.
Is G11.0 billable?
- Yes. G11.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G11.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G11.0 as a principal diagnosis.
Is G11.0 a CC or MCC?
- G11.0 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.