ICD-10-CM 2027
ICD-10 code for congenital honeycomb lung
From the official ICD-10-CM alphabetic index entry “Honeycomb lung › congenital”. Page updated September 29, 2026.
About coding congenital honeycomb lung
The ICD-10-CM code for congenital honeycomb lung is Q33.0 (Congenital cystic lung).
Within Q33 (congenital malformations of lung), Q33.0 is specifically for congenital cystic lung. Related codes cover accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), agenesis of lung (Q33.3), congenital bronchiectasis (Q33.4), ectopic tissue in lung (Q33.5), congenital hypoplasia and dysplasia of lung (Q33.6), other congenital malformations of lung (Q33.8) and congenital malformation of lung, unspecified (Q33.9).
Don't report Q33.0 together with the conditions in its Excludes1 note: cystic fibrosis (E84.0) and cystic lung disease, acquired or unspecified (J98.4).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for Q33.0)
Common questions about congenital honeycomb lung ICD-10 codes
What is the ICD-10 code for congenital honeycomb lung?
- Q33.0 — Congenital cystic lung.
Is Q33.0 billable?
- Yes. Q33.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q33.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q33.0 as a principal diagnosis.
Is Q33.0 a CC or MCC?
- Q33.0 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.