ICD-10 code for congenital central alveolar hypoventilation

The ICD-10-CM code for congenital central alveolar hypoventilation is G47.35 (Congenital central alveolar hypoventilation syndrome).

Within G47.3 (sleep apnea), G47.35 is specifically for congenital central alveolar hypoventilation syndrome. Related codes cover unspecified (G47.30), primary central sleep apnea (G47.31), high altitude periodic breathing (G47.32), obstructive sleep apnea (adult) (pediatric) (G47.33), idiopathic sleep related nonobstructive alveolar hypoventilation (G47.34), sleep related hypoventilation in conditions classified elsewhere (G47.36), central sleep apnea in conditions classified elsewhere (G47.37) and other sleep apnea (G47.39).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 011 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with MCC, relative weight 5.6154), DRG 012 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with CC, relative weight 4.381), DRG 013 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy without CC/MCC, relative weight 2.7307), DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in Pre-MDC and MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.