ICD-10-CM 2027
ICD-10 code for CINCA
From the official ICD-10-CM alphabetic index entry “CINCA (chronic infantile neurological, cutaneous and articular syndrome)”. Page updated September 29, 2026.
About coding CINCA
The ICD-10-CM code for CINCA is M04.2 (Cryopyrin-associated periodic syndromes).
Within M04 (autoinflammatory syndromes), M04.2 is specifically for Cryopyrin-associated periodic syndromes. Related codes cover periodic fever syndromes (M04.1), VEXAS syndrome (M04.3), other autoinflammatory syndromes (M04.8) and autoinflammatory syndrome, unspecified (M04.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 545 (Connective Tissue Disorders with MCC, relative weight 2.3892), DRG 546 (Connective Tissue Disorders with CC, relative weight 1.1745) and DRG 547 (Connective Tissue Disorders without CC/MCC, relative weight 0.7526), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about CINCA ICD-10 codes
What is the ICD-10 code for CINCA?
- M04.2 — Cryopyrin-associated periodic syndromes.
Is M04.2 billable?
- Yes. M04.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can M04.2 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict M04.2 as a principal diagnosis.
Is M04.2 a CC or MCC?
- No. M04.2 is neither a CC nor an MCC under MS-DRG v44.0.