ICD-10-CM 2027
ICD-10 code for CADASIL
Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy
From the official ICD-10-CM alphabetic index entry “CADASIL (cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy)”. Page updated September 29, 2026.
About coding CADASIL
The ICD-10-CM code for CADASIL is I67.850 (Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy).
Within I67.85 (hereditary cerebrovascular diseases), I67.850 is specifically for cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy. Related codes cover other hereditary cerebrovascular disease (I67.858).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 070 (Other Cerebrovascular Disorders with MCC, relative weight 1.6093), DRG 071 (Other Cerebrovascular Disorders with CC, relative weight 1.0177) and DRG 072 (Other Cerebrovascular Disorders without CC/MCC, relative weight 0.7348), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about CADASIL ICD-10 codes
What is the ICD-10 code for CADASIL?
- I67.850 — Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy.
Is I67.850 billable?
- Yes. I67.850 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I67.850 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I67.850 as a principal diagnosis.
Is I67.850 a CC or MCC?
- I67.850 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.