ICD-10-CM 2027
ICD-10 code for bullosa congenital epidermolysis
From the official ICD-10-CM alphabetic index entry “Epidermolysis › bullosa (congenital)”. Page updated September 29, 2026.
About coding bullosa congenital epidermolysis
The ICD-10-CM code for bullosa congenital epidermolysis is Q81.9 (Epidermolysis bullosa, unspecified). The official index lists 7 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q81.9.
Within Q81, choose Q81.9 (unspecified) only when documentation doesn't support a more specific option: simplex (Q81.0), letalis (Q81.1), dystrophica (Q81.2) and other epidermolysis bullosa (Q81.8).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 595 (Major Skin Disorders with MCC, relative weight 2.0239) and DRG 596 (Major Skin Disorders without MCC, relative weight 1.1071), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific bullosa congenital epidermolysis codes (official index)
- acquired L12.30 — Acquired epidermolysis bullosa, unspecified
- drug-induced L12.31 — Epidermolysis bullosa due to drug
- specified cause NEC L12.35 — Other acquired epidermolysis bullosa
- dystrophica Q81.2 — Epidermolysis bullosa dystrophica
- letalis Q81.1 — Epidermolysis bullosa letalis
- simplex Q81.0 — Epidermolysis bullosa simplex
- specified NEC Q81.8 — Other epidermolysis bullosa
Common questions about bullosa congenital epidermolysis ICD-10 codes
What is the ICD-10 code for bullosa congenital epidermolysis?
- Q81.9 — Epidermolysis bullosa, unspecified. More specific codes apply when the documentation supports them: L12.30, L12.31, L12.35, Q81.2 and others below.
What is the ICD-10 code for acquired bullosa congenital epidermolysis?
- L12.30 — Acquired epidermolysis bullosa, unspecified.
What is the ICD-10 code for dystrophica bullosa congenital epidermolysis?
- Q81.2 — Epidermolysis bullosa dystrophica.
What is the ICD-10 code for letalis bullosa congenital epidermolysis?
- Q81.1 — Epidermolysis bullosa letalis.
What is the ICD-10 code for simplex bullosa congenital epidermolysis?
- Q81.0 — Epidermolysis bullosa simplex.
Is Q81.9 billable?
- Yes. Q81.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q81.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q81.9 as a principal diagnosis.
Is Q81.9 a CC or MCC?
- No. Q81.9 is neither a CC nor an MCC under MS-DRG v44.0.