ICD-10 code for brain multiple malformation

The ICD-10-CM code for brain multiple malformation is Q04.9 (Congenital malformation of brain, unspecified). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q04.9.

Within Q04, choose Q04.9 (Congenital malformation of brain, unspecified) only when documentation doesn't support a more specific option: congenital malformations of corpus callosum (Q04.0), Arhinencephaly (Q04.1), holoprosencephaly (Q04.2), other reduction deformities of brain (Q04.3), Septo-optic dysplasia of brain (Q04.4), Megalencephaly (Q04.5), congenital cerebral cysts (Q04.6) and other specified congenital malformations of brain (Q04.8).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239), DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 01 (Diseases and Disorders of the Nervous System) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.