ICD-10-CM 2027
ICD-10 code for Biedl-Bardet syndrome
From the official ICD-10-CM alphabetic index entry “Biedl-Bardet syndrome”. Page updated September 29, 2026.
About coding Biedl-Bardet syndrome
The ICD-10-CM code for Biedl-Bardet syndrome is Q87.83 (Bardet-Biedl syndrome).
Within Q87.8 (other specified congenital malformation syndromes, not elsewhere classified), Q87.83 is specifically for Bardet-Biedl syndrome. Related codes cover Alport syndrome (Q87.81), arterial tortuosity syndrome (Q87.82), Laurence-Moon syndrome (Q87.84), MED13L syndrome (Q87.85), Kleefstra syndrome (Q87.86), Hao-Fountain Syndrome (Q87.87), CTNNB1 syndrome (Q87.88) and other specified congenital malformation syndromes, not elsewhere classified (Q87.89).
Use an additional code(s) to identify all associated manifestations.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about Biedl-Bardet syndrome ICD-10 codes
What is the ICD-10 code for Biedl-Bardet syndrome?
- Q87.83 — Bardet-Biedl syndrome.
Is Q87.83 billable?
- Yes. Q87.83 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q87.83 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q87.83 as a principal diagnosis.
Is Q87.83 a CC or MCC?
- Q87.83 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.