ICD-10-CM 2027
ICD-10 code for Arrhythmogenic right ventricular dysplasia
From the official ICD-10-CM alphabetic index entry “Dysplasia › arrhythmogenic right ventricular”. Page updated September 29, 2026.
About coding Arrhythmogenic right ventricular dysplasia
The ICD-10-CM code for Arrhythmogenic right ventricular dysplasia is I42.81 (Arrhythmogenic cardiomyopathy).
Within I42.8 (other cardiomyopathies), I42.81 is specifically for Arrhythmogenic cardiomyopathy. Related codes cover not elsewhere classified (I42.89).
Code first: pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about Arrhythmogenic right ventricular dysplasia ICD-10 codes
What is the ICD-10 code for Arrhythmogenic right ventricular dysplasia?
- I42.81 — Arrhythmogenic cardiomyopathy.
Is I42.81 billable?
- Yes. I42.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I42.81 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I42.81 as a principal diagnosis.
Is I42.81 a CC or MCC?
- I42.81 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.