ICD-10-CM 2027
ICD-10 code for Arrhythmogenic cardiomyopathy
From the official ICD-10-CM alphabetic index entry “Cardiomyopathy (familial) (idiopathic) › arrhythmogenic”. Page updated September 29, 2026.
About coding Arrhythmogenic cardiomyopathy
The ICD-10-CM code for Arrhythmogenic cardiomyopathy is I42.81 (Arrhythmogenic cardiomyopathy). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on I42.81.
Within I42.8 (other cardiomyopathies), I42.81 is specifically for Arrhythmogenic cardiomyopathy. Related codes cover not elsewhere classified (I42.89).
Code first: pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
More specific Arrhythmogenic cardiomyopathy codes (official index)
Common questions about Arrhythmogenic cardiomyopathy ICD-10 codes
What is the ICD-10 code for Arrhythmogenic cardiomyopathy?
- I42.81 — Arrhythmogenic cardiomyopathy. More specific codes apply when the documentation supports them: I42.81, I42.81.
What is the ICD-10 code for biventricular arrhythmogenic cardiomyopathy?
- I42.81 — Arrhythmogenic cardiomyopathy.
What is the ICD-10 code for ventricular arrhythmogenic cardiomyopathy?
- I42.81 — Arrhythmogenic cardiomyopathy.
Is I42.81 billable?
- Yes. I42.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I42.81 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I42.81 as a principal diagnosis.
Is I42.81 a CC or MCC?
- I42.81 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.