ICD-10-CM 2027
ICD-10 code for Alport syndrome
From the official ICD-10-CM alphabetic index entry “Alport syndrome”. Page updated September 29, 2026.
About coding Alport syndrome
The ICD-10-CM code for Alport syndrome is Q87.81 (Alport syndrome).
Within Q87.8 (other specified congenital malformation syndromes, not elsewhere classified), Q87.81 is specifically for Alport syndrome. Related codes cover arterial tortuosity syndrome (Q87.82), Bardet-Biedl syndrome (Q87.83), Laurence-Moon syndrome (Q87.84), MED13L syndrome (Q87.85), Kleefstra syndrome (Q87.86), Hao-Fountain Syndrome (Q87.87), CTNNB1 syndrome (Q87.88) and other specified congenital malformation syndromes, not elsewhere classified (Q87.89).
Use an additional code to identify stage of chronic kidney disease (N18.1-N18.6). Use an additional code(s) to identify all associated manifestations.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about Alport syndrome ICD-10 codes
What is the ICD-10 code for Alport syndrome?
- Q87.81 — Alport syndrome.
Is Q87.81 billable?
- Yes. Q87.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q87.81 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q87.81 as a principal diagnosis.
Is Q87.81 a CC or MCC?
- Q87.81 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.