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ICD-10-CM 2027

ICD-10 code for agenesis

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Agenesis”. Page updated September 29, 2026.

About coding agenesis

The official ICD-10-CM index doesn't give a single default code for agenesis; the code depends on the details below.

More specific agenesis codes (official index)

  • adrenal (gland) Q89.1 — Congenital malformations of adrenal gland
  • alimentary tract (complete) (partial) NEC Q45.8 — Other specified congenital malformations of digestive system
  • upper Q40.8 — Other specified congenital malformations of upper alimentary tract
  • anus, anal (canal) Q42.3 — Congenital absence, atresia and stenosis of anus without fistula
  • with fistula Q42.2 — Congenital absence, atresia and stenosis of anus with fistula
  • aorta Q25.41 — Absence and aplasia of aorta
  • appendix Q42.8 — Congenital absence, atresia and stenosis of other parts of large intestine
  • arm (complete) Q71.0 — Congenital complete absence of upper limb
  • with hand present Q71.1 — Congenital absence of upper arm and forearm with hand present
  • artery (peripheral) Q27.9 — Congenital malformation of peripheral vascular system, unspecified
  • brain Q28.3 — Other malformations of cerebral vessels
  • coronary Q24.5 — Malformation of coronary vessels
  • pulmonary Q25.79 — Other congenital malformations of pulmonary artery
  • specified NEC Q27.8 — Other specified congenital malformations of peripheral vascular system
  • umbilical Q27.0 — Congenital absence and hypoplasia of umbilical artery
  • auditory (canal) (external) Q16.1 — Congenital absence, atresia and stricture of auditory canal (external)
  • auricle (ear) Q16.0 — Congenital absence of (ear) auricle
  • bile duct or passage Q44.5 — Other congenital malformations of bile ducts
  • bladder Q64.5 — Congenital absence of bladder and urethra
  • bone Q79.9 — Congenital malformation of musculoskeletal system, unspecified
  • brain Q00.0 — Anencephaly
  • part of Q04.3 — Other reduction deformities of brain
  • breast (with nipple present) Q83.8 — Other congenital malformations of breast
  • with absent nipple Q83.0 — Congenital absence of breast with absent nipple
  • bronchus Q32.4 — Other congenital malformations of bronchus
  • canaliculus lacrimalis Q10.4 — Absence and agenesis of lacrimal apparatus
  • carpus
  • cartilage Q79.9 — Congenital malformation of musculoskeletal system, unspecified
  • cecum Q42.8 — Congenital absence, atresia and stenosis of other parts of large intestine
  • cerebellum Q04.3 — Other reduction deformities of brain
  • cervix Q51.5 — Agenesis and aplasia of cervix
  • chin Q18.8 — Other specified congenital malformations of face and neck
  • cilia Q10.3 — Other congenital malformations of eyelid
  • circulatory system, part NOS Q28.9 — Congenital malformation of circulatory system, unspecified
  • clavicle Q74.0 — Other congenital malformations of upper limb(s), including shoulder girdle
  • clitoris Q52.6 — Congenital malformation of clitoris
  • coccyx Q76.49 — Other congenital malformations of spine, not associated with scoliosis
  • colon Q42.9 — Congenital absence, atresia and stenosis of large intestine, part unspecified
  • specified NEC Q42.8 — Congenital absence, atresia and stenosis of other parts of large intestine
  • corpus callosum Q04.0 — Congenital malformations of corpus callosum
  • cricoid cartilage Q31.8 — Other congenital malformations of larynx
  • diaphragm (with hernia) Q79.1 — Other congenital malformations of diaphragm
  • digestive organ (s) or tract (complete) (partial) NEC Q45.8 — Other specified congenital malformations of digestive system
  • upper Q40.8 — Other specified congenital malformations of upper alimentary tract
  • ductus arteriosus Q28.8 — Other specified congenital malformations of circulatory system
  • duodenum Q41.0 — Congenital absence, atresia and stenosis of duodenum
  • ear Q16.9 — Congenital malformation of ear causing impairment of hearing, unspecified
  • auricle Q16.0 — Congenital absence of (ear) auricle
  • lobe Q17.8 — Other specified congenital malformations of ear
  • ejaculatory duct Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • endocrine (gland) NEC Q89.2 — Congenital malformations of other endocrine glands
  • epiglottis Q31.8 — Other congenital malformations of larynx
  • esophagus Q39.8 — Other congenital malformations of esophagus
  • eustachian tube Q16.2 — Absence of eustachian tube
  • eye Q11.1 — Other anophthalmos
  • adnexa Q15.8 — Other specified congenital malformations of eye
  • eyelid (fold) Q10.3 — Other congenital malformations of eyelid
  • face
  • bones NEC Q75.8 — Other specified congenital malformations of skull and face bones
  • specified part NEC Q18.8 — Other specified congenital malformations of face and neck
  • fallopian tube Q50.6 — Other congenital malformations of fallopian tube and broad ligament
  • femur
  • fibula
  • finger (complete) (partial)
  • foot (and toes) (complete) (partial) Q72.3 — Congenital absence of foot and toe(s)
  • forearm (with hand present)
  • and hand Q71.2 — Congenital absence of both forearm and hand
  • gallbladder Q44.0 — Agenesis, aplasia and hypoplasia of gallbladder
  • gastric Q40.2 — Other specified congenital malformations of stomach
  • genitalia, genital (organ(s))
  • female Q52.8 — Other specified congenital malformations of female genitalia
  • external Q52.71 — Congenital absence of vulva
  • internal NEC Q52.8 — Other specified congenital malformations of female genitalia
  • male Q55.8 — Other specified congenital malformations of male genital organs
  • glottis Q31.8 — Other congenital malformations of larynx
  • hair Q84.0 — Congenital alopecia
  • hand (and fingers) (complete) (partial) Q71.3 — Congenital absence of hand and finger
  • heart Q24.8 — Other specified congenital malformations of heart
  • valve NEC Q24.8 — Other specified congenital malformations of heart
  • pulmonary Q22.0 — Pulmonary valve atresia
  • hepatic Q44.79 — Other congenital malformations of liver
  • humerus
  • hymen Q52.4 — Other congenital malformations of vagina
  • ileum Q41.2 — Congenital absence, atresia and stenosis of ileum
  • incus Q16.3 — Congenital malformation of ear ossicles
  • intestine (small) Q41.9 — Congenital absence, atresia and stenosis of small intestine, part unspecified
  • large Q42.9 — Congenital absence, atresia and stenosis of large intestine, part unspecified
  • specified NEC Q42.8 — Congenital absence, atresia and stenosis of other parts of large intestine
  • iris (dilator fibers) Q13.1 — Absence of iris
  • jaw M26.09 — Other specified anomalies of jaw size
  • jejunum Q41.1 — Congenital absence, atresia and stenosis of jejunum
  • kidney (s) (partial) Q60.2 — Renal agenesis, unspecified
  • bilateral Q60.1 — Renal agenesis, bilateral
  • unilateral Q60.0 — Renal agenesis, unilateral
  • labium (majus) (minus) Q52.71 — Congenital absence of vulva
  • labyrinth, membranous Q16.5 — Congenital malformation of inner ear
  • lacrimal apparatus Q10.4 — Absence and agenesis of lacrimal apparatus
  • larynx Q31.8 — Other congenital malformations of larynx
  • leg (complete) Q72.0 — Congenital complete absence of lower limb
  • with foot present Q72.1 — Congenital absence of thigh and lower leg with foot present
  • lower leg (with foot present)
  • and foot Q72.2 — Congenital absence of both lower leg and foot
  • lens Q12.3 — Congenital aphakia
  • limb (complete) Q73.0 — Congenital absence of unspecified limb(s)
  • lower
  • upper
  • lip Q38.0 — Congenital malformations of lips, not elsewhere classified
  • liver Q44.79 — Other congenital malformations of liver
  • lung (fissure) (lobe) (bilateral) (unilateral) Q33.3 — Agenesis of lung
  • mandible, maxilla M26.09 — Other specified anomalies of jaw size
  • metacarpus
  • metatarsus
  • muscle Q79.8 — Other congenital malformations of musculoskeletal system
  • eyelid Q10.3 — Other congenital malformations of eyelid
  • ocular Q15.8 — Other specified congenital malformations of eye
  • musculoskeletal system NEC Q79.8 — Other congenital malformations of musculoskeletal system
  • nail (s) Q84.3 — Anonychia
  • neck, part Q18.8 — Other specified congenital malformations of face and neck
  • nerve Q07.8 — Other specified congenital malformations of nervous system
  • nervous system, part NEC Q07.8 — Other specified congenital malformations of nervous system
  • nipple Q83.2 — Absent nipple
  • nose Q30.1 — Agenesis and underdevelopment of nose
  • nuclear Q07.8 — Other specified congenital malformations of nervous system
  • organ
  • of Corti Q16.5 — Congenital malformation of inner ear
  • or site not listed
  • osseous meatus (ear) Q16.1 — Congenital absence, atresia and stricture of auditory canal (external)
  • ovary
  • bilateral Q50.02 — Congenital absence of ovary, bilateral
  • unilateral Q50.01 — Congenital absence of ovary, unilateral
  • oviduct Q50.6 — Other congenital malformations of fallopian tube and broad ligament
  • pancreas Q45.0 — Agenesis, aplasia and hypoplasia of pancreas
  • parathyroid (gland) Q89.2 — Congenital malformations of other endocrine glands
  • parotid gland (s) Q38.4 — Congenital malformations of salivary glands and ducts
  • patella Q74.1 — Congenital malformation of knee
  • pelvic girdle (complete) (partial) Q74.2 — Other congenital malformations of lower limb(s), including pelvic girdle
  • penis Q55.5 — Congenital absence and aplasia of penis
  • pericardium Q24.8 — Other specified congenital malformations of heart
  • pituitary (gland) Q89.2 — Congenital malformations of other endocrine glands
  • prostate Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • punctum lacrimale Q10.4 — Absence and agenesis of lacrimal apparatus
  • radioulnar
  • radius
  • rectum Q42.1 — Congenital absence, atresia and stenosis of rectum without fistula
  • with fistula Q42.0 — Congenital absence, atresia and stenosis of rectum with fistula
  • renal Q60.2 — Renal agenesis, unspecified
  • bilateral Q60.1 — Renal agenesis, bilateral
  • unilateral Q60.0 — Renal agenesis, unilateral
  • respiratory organ NEC Q34.8 — Other specified congenital malformations of respiratory system
  • rib Q76.6 — Other congenital malformations of ribs
  • roof of orbit Q75.8 — Other specified congenital malformations of skull and face bones
  • round ligament Q52.8 — Other specified congenital malformations of female genitalia
  • sacrum Q76.49 — Other congenital malformations of spine, not associated with scoliosis
  • salivary gland Q38.4 — Congenital malformations of salivary glands and ducts
  • scapula Q74.0 — Other congenital malformations of upper limb(s), including shoulder girdle
  • scrotum Q55.29 — Other congenital malformations of testis and scrotum
  • seminal vesicles Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • septum
  • atrial Q21.19 — Other specified atrial septal defect
  • between aorta and pulmonary artery Q21.4 — Aortopulmonary septal defect
  • ventricular Q20.4 — Double inlet ventricle
  • shoulder girdle (complete) (partial) Q74.0 — Other congenital malformations of upper limb(s), including shoulder girdle
  • skull (bone) Q75.8 — Other specified congenital malformations of skull and face bones
  • with
  • anencephaly Q00.0 — Anencephaly
  • encephalocele
  • hydrocephalus Q03.9 — Congenital hydrocephalus, unspecified
  • with spina bifida
  • microcephaly Q02 — Microcephaly
  • spermatic cord Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • spinal cord Q06.0 — Amyelia
  • spine Q76.49 — Other congenital malformations of spine, not associated with scoliosis
  • spleen Q89.01 — Asplenia (congenital)
  • sternum Q76.7 — Congenital malformation of sternum
  • stomach Q40.2 — Other specified congenital malformations of stomach
  • submaxillary gland (s) (congenital) Q38.4 — Congenital malformations of salivary glands and ducts
  • tarsus
  • tendon Q79.8 — Other congenital malformations of musculoskeletal system
  • testicle Q55.0 — Absence and aplasia of testis
  • thymus (gland) Q89.2 — Congenital malformations of other endocrine glands
  • thyroid (gland) E03.1 — Congenital hypothyroidism without goiter
  • cartilage Q31.8 — Other congenital malformations of larynx
  • tibia
  • tibiofibular
  • toe (and foot) (complete) (partial)
  • tongue Q38.3 — Other congenital malformations of tongue
  • trachea (cartilage) Q32.1 — Other congenital malformations of trachea
  • ulna
  • upper limb
  • ureter Q62.4 — Agenesis of ureter
  • urethra Q64.5 — Congenital absence of bladder and urethra
  • urinary tract NEC Q64.8 — Other specified congenital malformations of urinary system
  • uterus Q51.0 — Agenesis and aplasia of uterus
  • uvula Q38.5 — Congenital malformations of palate, not elsewhere classified
  • vagina Q52.0 — Congenital absence of vagina
  • vas deferens Q55.4 — Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  • vein (s) (peripheral) Q27.9 — Congenital malformation of peripheral vascular system, unspecified
  • brain Q28.3 — Other malformations of cerebral vessels
  • great NEC Q26.8 — Other congenital malformations of great veins
  • portal Q26.5 — Anomalous portal venous connection
  • vena cava (inferior) (superior) Q26.8 — Other congenital malformations of great veins
  • vermis of cerebellum Q04.3 — Other reduction deformities of brain
  • vertebra Q76.49 — Other congenital malformations of spine, not associated with scoliosis
  • vulva Q52.71 — Congenital absence of vulva

Common questions about agenesis ICD-10 codes

What is the ICD-10 code for adrenal agenesis?

Q89.1 — Congenital malformations of adrenal gland.

What is the ICD-10 code for alimentary tract nec agenesis?

Q45.8 — Other specified congenital malformations of digestive system.

What is the ICD-10 code for aorta agenesis?

Q25.41 — Absence and aplasia of aorta.

What is the ICD-10 code for appendix agenesis?

Q42.8 — Congenital absence, atresia and stenosis of other parts of large intestine.

What is the ICD-10 code for arm agenesis?

Q71.0 — Congenital complete absence of upper limb (header code; choose a more specific subcode).

What is the ICD-10 code for artery agenesis?

Q27.9 — Congenital malformation of peripheral vascular system, unspecified.

What is the ICD-10 code for auditory agenesis?

Q16.1 — Congenital absence, atresia and stricture of auditory canal (external).